The case of an 11-year-old boy with hypermetropia of +22.0 diopters is reported. Axial length was only 14.8 mm. The features and extreme rarity of this variation in the shape of the globe is outlined. The dimensions of the eyeball were measured by echography and compared to the emmetropic eye of the adult. Only vitreous length was found to be shortened, while the dimensions of the anterior segment were within normal limits. The term posterior microphthalmos without microcornea was chosen. Associated pseudopapilledema and choroidal folds were found. The literature is reviewed.