In vitro fibroblast studies in a patient with C6-C10-dicarboxylic aciduria: evidence for a defect in general acyl-CoA dehydrogenase

Clin Chim Acta. 1982 Nov 24;126(1):53-67. doi: 10.1016/0009-8981(82)90361-8.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acyl-CoA Dehydrogenases / metabolism*
  • Apoenzymes / metabolism*
  • Apoproteins / metabolism*
  • Cells, Cultured
  • Child
  • Child, Preschool
  • Dicarboxylic Acids / urine*
  • Fatty Acids / metabolism*
  • Fibroblasts / enzymology
  • Humans
  • Lipid Metabolism, Inborn Errors / enzymology*
  • Lipid Metabolism, Inborn Errors / urine
  • Oxidation-Reduction

Substances

  • Apoenzymes
  • Apoproteins
  • Dicarboxylic Acids
  • Fatty Acids
  • Acyl-CoA Dehydrogenases