Abstract
The case of a 40-year-old patient with Dejerine-Sottas disease, who developed spinal cord compression from hypertrophic nerve roots, is presented. Six previously reported cases are reviewed. We discuss the characteristic myelographic changes seen in Dejerine-Sottas disease.
MeSH terms
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Adult
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Biopsy
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Humans
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Hypertrophy
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Male
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Motor Neurons* / ultrastructure
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Myelography
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Neural Conduction
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Neuromuscular Diseases / complications*
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Neuromuscular Diseases / diagnostic imaging
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Neuromuscular Diseases / genetics
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Peroneal Nerve / pathology
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Spinal Cord Compression / diagnostic imaging*
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Spinal Nerve Roots / pathology*