Skip to main page content
Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
, 30 (3), 331-4

Sydenham Chorea: An Update

Sydenham Chorea: An Update

P A Nausieda et al. Neurology.


To document possible changing characteristics of Sydenham chorea, we reviewed records of 240 patients with this diagnosis who were seen between 1951 and 1976. A dramatic progressive decline in the number of cases was observed. The syndrome occurred mainly in childhood. Female predominance was apparent only after the 10. There was a high femilial incidence for both chorea and rheumatic fever. Most patients had generalized chorea, and fewer than 20% had hemichorea. Dysarthria, probably of extrapyramidal origin, was frequent but neurologic abnormalities other than diffuse encephalopathy were rare. One-third of the patients had coexisting heart disease. Repeat attacks of Sydenham chorea occurred, but the recurrence rate was much less than noted in previous studies.

Similar articles

  • Sydenham Chorea: Clinical and Laboratory Findings. Analysis of 187 Cases
    J Goldenberg et al. Rev Paul Med 110 (4), 152-7. PMID 1341004.
    Sydenham's chorea (chorea minor, St. Vitus dance, rheumatic encephalitis), described by Thomas Sydenham in 1686, is considered one of the major manifestations of rheumati …
  • Chorea as a Manifestation of Rheumatic Fever--A 30-year Survey (1960-1990)
    G Eshel et al. Eur J Pediatr 152 (8), 645-6. PMID 8404967.
    Sydenham chorea, a major manifestation of acute rheumatic fever, has been the most common form of acquired chorea during childhood. Despite the recent dramatic decline in …
  • Sydenham's Chorea
    ML Kulkarni et al. Indian Pediatr 33 (2), 112-5. PMID 8772928.
    There was an increased incidence of Sydenham's chorea after 9 years of age in girls possibly suggesting the influence of female sex hormones. A high incidence of neurolog …
  • Benign Hereditary Chorea
    PG Wheeler et al. Pediatr Neurol 9 (5), 337-40. PMID 8292207. - Review
    Benign hereditary chorea is an uncommon inherited form of childhood chorea that can be mistaken for much more serious disorders, such as Huntington disease. The clinical …
  • [Sydenham Rheumatic Chorea]
    J Rodríguez Ormazabal. Rev Neurol 23 Suppl 3, S334-8. PMID 7497310. - Review
See all similar articles

Cited by 13 PubMed Central articles

See all "Cited by" articles

LinkOut - more resources