Role of argininosuccinate synthetase in the regulation of urea synthesis in the rat and argininosuccinate synthetase-associated metabolic disorder in man

Adv Enzyme Regul. 1980:18:221-38. doi: 10.1016/0065-2571(80)90017-5.
No abstract available

MeSH terms

  • Adult
  • Amino Acid Metabolism, Inborn Errors / enzymology*
  • Ammonium Chloride / pharmacology
  • Animals
  • Argininosuccinate Synthase / deficiency
  • Argininosuccinate Synthase / metabolism*
  • Citrulline / blood*
  • Dietary Proteins / administration & dosage
  • Female
  • Glutamates / metabolism
  • Humans
  • Ligases / metabolism*
  • Liver / drug effects
  • Liver / enzymology
  • Liver / metabolism
  • Male
  • Middle Aged
  • Ornithine / metabolism
  • Rats
  • Urea / biosynthesis*

Substances

  • Dietary Proteins
  • Glutamates
  • Ammonium Chloride
  • Citrulline
  • Urea
  • Ornithine
  • Ligases
  • Argininosuccinate Synthase