Restrictive cardiomyopathy in pseudoxanthoma elasticum

Chest. 1980 Jul;78(1):113-5. doi: 10.1378/chest.78.1.113.


A unique case of severe and diffuse endocardial fibroelastosis covering the entire left ventricle and associated with pseudoxanthoma elasticum is presented. The clinical picture was that of an apparently primary restrictive cardiomyopathy. Specific histologic lesions could be recognized in the endocardium.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Cardiomyopathies / etiology*
  • Cardiomyopathies / pathology
  • Endocardial Fibroelastosis / etiology
  • Endocardial Fibroelastosis / pathology
  • Female
  • Humans
  • Pseudoxanthoma Elasticum / complications*
  • Pseudoxanthoma Elasticum / pathology