Liver disease in cystic fibrosis

Arch Dis Child. 1995 Apr;72(4):281-4. doi: 10.1136/adc.72.4.281.
No abstract available

Publication types

  • Review

MeSH terms

  • Adolescent
  • Adult
  • Bile Duct Diseases / complications
  • Cystic Fibrosis / complications*
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Disease Susceptibility
  • Genetic Therapy
  • Humans
  • Liver Diseases / etiology*
  • Liver Diseases / metabolism
  • Liver Diseases / therapy
  • Membrane Proteins / analysis
  • Ursodeoxycholic Acid / therapeutic use

Substances

  • CFTR protein, human
  • Membrane Proteins
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Ursodeoxycholic Acid