Unchanged MRI of myelin in adolescents with PKU supplied with non-phe essential amino acids after dietary relaxation

Acta Paediatr. 1994 Dec;83(12):1312-4. doi: 10.1111/j.1651-2227.1994.tb13025.x.
No abstract available

MeSH terms

  • Adolescent
  • Amino Acids, Essential / administration & dosage*
  • Amino Acids, Essential / blood
  • Brain / pathology*
  • Female
  • Follow-Up Studies
  • Humans
  • Magnetic Resonance Imaging*
  • Male
  • Myelin Proteins / metabolism*
  • Myelin Sheath / pathology*
  • Phenylalanine / administration & dosage
  • Phenylalanine / blood
  • Phenylketonurias / blood
  • Phenylketonurias / diagnosis
  • Phenylketonurias / diet therapy*

Substances

  • Amino Acids, Essential
  • Myelin Proteins
  • Phenylalanine