[Multiple entrapments neuropathy in adult polyglucosan body disease]

Neurologia. 1995 Apr;10(4):167-70.
[Article in Spanish]

Abstract

Adult polyglucosan body disease (APBD) is a rare condition characterized by neuropathy, dementia, upper motor neuron dysfunction and neurogenic bladder. For diagnosis, the presence of polyglucosan bodies (PB), or PAS (+) glucose polymers, must be demonstrated. In this description of a woman with APBD and multiple entrapment neuropathy, we discuss a possible role for morphological changes induced by PB in increasing susceptibility to pressure palsies.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Demyelinating Diseases / complications
  • Female
  • Glucans / analysis*
  • Humans
  • Median Nerve / physiopathology*
  • Middle Aged
  • Nerve Compression Syndromes / complications
  • Nerve Compression Syndromes / diagnosis*
  • Nerve Compression Syndromes / physiopathology
  • Neural Conduction
  • Peroneal Nerve / physiopathology*
  • Radial Nerve / physiopathology*
  • Sural Nerve / chemistry
  • Sural Nerve / physiopathology*
  • Tibial Nerve / physiopathology*

Substances

  • Glucans