Extradural tumor causing spinal cord compression in Klippel-Trenaunay-Weber syndrome

Surg Neurol. 1995 Mar;43(3):257-60. doi: 10.1016/0090-3019(95)80009-6.


Background: Myelopathy in Klippel-Trenaunay-Weber syndrome is uncommon but has been reported secondary to spinal vascular malformations.

Report: A patient with Klippel-Trenaunay-Weber syndrome who presented with spinal cord compression from a spinal extradural mass lesion (angiomyolipoma) is described.

Discussion: This association has not been reported previously but is consistent with the segmental vascular abnormalities observed in Klippel-Trenaunay-Weber syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Angiomyolipoma / complications*
  • Angiomyolipoma / etiology
  • Angiomyolipoma / pathology
  • Diagnosis, Differential
  • Dura Mater
  • Humans
  • Klippel-Trenaunay-Weber Syndrome / complications*
  • Klippel-Trenaunay-Weber Syndrome / pathology
  • Magnetic Resonance Imaging
  • Male
  • Spinal Cord Compression / etiology*
  • Spinal Cord Compression / pathology
  • Spinal Cord Neoplasms / complications*
  • Spinal Cord Neoplasms / etiology
  • Spinal Cord Neoplasms / pathology