Choristoma of the intracranial maxillary nerve in a child. Case report

J Neurosurg. 1994 Nov;81(5):788-91. doi: 10.3171/jns.1994.81.5.0788.


This report describes what the authors believe to be the first reported case of choristoma of the intracranial maxillary nerve. This 12-year-old girl presented with a 5-year history of severe isolated left-sided trigeminal neuralgia. Computerized tomography and magnetic resonance imaging revealed a mass below the anterior portion of the left cavernous sinus, enlarging the foramen rotundum. Total resection was achieved via a pterional extradural approach. Histological examination revealed a choristoma composed of smooth-muscle fibers. The histogenesis of these tumors when they develop in a nerve remains unclear. They may represent abnormal migration or proliferation of neuroectodermal tissue in or close to a peripheral nerve. Total removal of these tumors should be attempted at initial diagnosis.

Publication types

  • Case Reports

MeSH terms

  • Actin Cytoskeleton / pathology
  • Cavernous Sinus / innervation*
  • Child
  • Choristoma / complications
  • Choristoma / pathology*
  • Cranial Nerve Diseases / pathology
  • Female
  • Humans
  • Maxillary Nerve / pathology*
  • Muscle Fibers, Skeletal / pathology*
  • Muscle, Smooth / pathology*
  • Trigeminal Ganglion / pathology
  • Trigeminal Neuralgia / etiology