Intra-abdominal desmoplastic small round-cell tumor in a postmenopausal female. Report of a case and review of the literature

Abstract

Intra-abdominal desmoplastic small round cell tumor is a rare malignancy which tends to occur in adolescent males. Fewer than 30 cases of this malignancy have been described, and long term survival is poor. We present a case of intra-abdominal desmoplastic small round cell tumor occurring in a post-menopausal woman that mimicked ovarian carcinoma. The clinicopathologic features and literature are reviewed.