Blue rubber bleb nevi are histologically benign vascular neoplasms of the skin and gastrointestinal tract, which may cause pain and limb-threatening deformities, as well as potentially fatal visceral hemorrhage. Treatment of cutaneous and soft tissue lesions includes local excision, aimed at symptomatic relief, with appropriate referral for evaluation of gastrointestinal lesions and secondary anemia. A case of blue rubber bleb nevus syndrome with lesions of the foot is reported.