Pulmonary hypertension associated with portal hypertension in a child with Williams syndrome--a case report

Pediatr Pathol. 1994 Jan-Feb;14(1):61-8. doi: 10.3109/15513819409022026.

Abstract

A 14-year-old white female with Williams syndrome and portal hypertension presented in shock; at autopsy she was found to have grade II to VI vascular changes of pulmonary hypertension. This case demonstrates the association of portal hypertension and pulmonary hypertension in a pediatric patient.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Abnormalities, Multiple / physiopathology
  • Adolescent
  • Female
  • Humans
  • Hypertension, Portal / complications*
  • Hypertension, Pulmonary / complications*
  • Syndrome