Animal model of human disease: GM2 gangliosidosis

Am J Pathol. 1976 May;83(2):419-22.
No abstract available

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Cytoplasmic Granules / ultrastructure
  • Disease Models, Animal*
  • G(M2) Ganglioside
  • Gangliosidoses / enzymology
  • Gangliosidoses / genetics
  • Gangliosidoses / pathology*
  • Hexosaminidases / analysis
  • Hexosaminidases / deficiency
  • Humans
  • Swine
  • Swine Diseases / pathology*

Substances

  • G(M2) Ganglioside
  • Hexosaminidases