[Anesthetic management of a patient with a cryptophthalmos syndactyly syndrome and subglottic stenosis]

Masui. 1994 Mar;43(3):415-7.
[Article in Japanese]


We experienced five episodes of anesthesia for a girl with dryptophthalmos syndactyly syndrome and congenital subglottic stenosis from the age of 1.3 year to 4 years. A girl was born at 34 weeks of gestation. The birth weight was 1360 g. The Apgar score was 8 at one minute and there was a hoarseness. She had right cryptophthalmos, syndactyly of hands and left foot, left polydactyly, anomalies of ear and nose, and agenesis of right kidney. The operation was scheduled for syndactyly under general anesthesia when she was 17 days and 5 months. As intubation was unsuccessful in both occasions, the operation was cancelled and subglottic stenosis was pointed out. We decided to postpone the operation until she could cry fully without cyanosis. We evaluated her respiratory ability from the time she became able to cry fully without cyanosis. As a result, we could manage her without any complications such as hypoxia or hypercapnea except mild wheezing.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Abnormalities, Multiple*
  • Anesthesia, General / methods*
  • Anophthalmos
  • Child, Preschool
  • Eyelids / abnormalities*
  • Female
  • Glottis
  • Humans
  • Infant
  • Infant, Newborn
  • Laryngostenosis / congenital*
  • Syndactyly / surgery*
  • Syndrome