Abstract
We report a family suffering from dominant dystrophic epidermolysis bullosa, in whom linear lichenified lesions and troublesome pruritus were prominent features. We consider that this clinical picture may constitute a separate subtype of this disorder.
MeSH terms
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Adult
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Diagnosis, Differential
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Epidermolysis Bullosa Dystrophica / complications*
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Epidermolysis Bullosa Dystrophica / pathology
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Family
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Female
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Humans
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Leg
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Prurigo / complications*
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Prurigo / pathology
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Skin / pathology
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Skin / ultrastructure