The Niemann-Pick C lesion and its relationship to the intracellular distribution and utilization of LDL cholesterol

Biochim Biophys Acta. 1994 Feb 22;1225(3):235-43. doi: 10.1016/0925-4439(94)90001-9.
No abstract available

Publication types

  • Review

MeSH terms

  • Animals
  • Biological Transport
  • Cholesterol / metabolism
  • Cholesterol Esters / metabolism
  • Cholesterol, LDL / metabolism*
  • Fibroblasts / metabolism
  • Humans
  • Liver / metabolism
  • Niemann-Pick Diseases / etiology*
  • Niemann-Pick Diseases / metabolism
  • Receptors, LDL / metabolism*
  • Subcellular Fractions / metabolism

Substances

  • Cholesterol Esters
  • Cholesterol, LDL
  • Receptors, LDL
  • Cholesterol