Langerhans' cell histiocytosis presenting with the superior vena cava syndrome: a case report

Med Pediatr Oncol. 1993;21(6):456-9. doi: 10.1002/mpo.2950210614.


A case of Langerhans' cell histiocytosis confined to the mediastinum and presenting with de novo superior cava syndrome is reported. The causes of superior vena cava syndrome in childhood are discussed as is the importance of obtaining pathologic diagnosis prior to initiating therapy.

Publication types

  • Case Reports

MeSH terms

  • Diagnosis, Differential
  • Female
  • Histiocytosis, Langerhans-Cell / complications
  • Histiocytosis, Langerhans-Cell / diagnosis*
  • Humans
  • Infant
  • Superior Vena Cava Syndrome / etiology*