MRI of white matter changes in the Sjögren-Larsson syndrome

Neuroradiology. 1995 Oct;37(7):576-7. doi: 10.1007/BF00593725.


We report a case of Sjögren-Larsson syndrome with spastic diplegia and conduction aphasia. MRI demonstrated the white matter changes deep in the cerebral hemispheres. We analyse the MRI findings and compare the results with neuropsychological signs.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Aphasia, Conduction / diagnosis
  • Brain / pathology*
  • Cerebral Palsy / diagnosis
  • Humans
  • Magnetic Resonance Imaging*
  • Male
  • Nerve Fibers / pathology
  • Neurologic Examination
  • Neuropsychological Tests
  • Sjogren-Larsson Syndrome / diagnosis*