Coexisting extraadrenal pheochromocytoma and renal artery stenosis: a case report and review of the pathophysiology

J Pediatr Surg. 1995 Nov;30(11):1613-5. doi: 10.1016/0022-3468(95)90172-8.

Abstract

The authors report the case of an 8-year-old boy with coexisting malignant extraadrenal pheochromocytoma and ipsilateral renal artery stenosis, severe hypertension, normal urinary vanillylmandelic acid levels, and elevated catecholamines and renin levels. Reported mechanisms of the stenosis are reviewed. The interrelationships of catecholamines, renin, and angiotensin and their effects on renal vasculature are discussed.

Publication types

  • Case Reports

MeSH terms

  • Catecholamines / metabolism
  • Child
  • Humans
  • Hypertension, Renovascular / etiology
  • Hypertension, Renovascular / metabolism
  • Hypertension, Renovascular / physiopathology
  • Kidney Neoplasms / complications*
  • Kidney Neoplasms / physiopathology
  • Male
  • Paraganglioma, Extra-Adrenal / complications*
  • Paraganglioma, Extra-Adrenal / physiopathology
  • Pheochromocytoma / complications*
  • Pheochromocytoma / physiopathology
  • Renal Artery Obstruction / complications*
  • Renal Artery Obstruction / physiopathology
  • Renin / blood
  • Vanilmandelic Acid / urine

Substances

  • Catecholamines
  • Vanilmandelic Acid
  • Renin