Purpose: To report the presence of posterior segment neovascularization in eyes with optic nerve aplasia.
Methods: Three eyes in two patients with clinical optic nerve aplasia were studied.
Results: Examination disclosed posterior segment neovascularization in one eye and progressive posterior segment neovascularization in two eyes.
Conclusions: Posterior segment neovascularization may occur in association with optic nerve aplasia. Retinal ischemia or retinochoroidal anatomic disorganization, or both, may provide the stimulus for neovascularization in such eyes.