Accessory hepatic vein to pulmonary venous atrium as a cause of cyanosis after the Fontan operation

Am J Cardiol. 1996 Jun 15;77(15):1386-7. doi: 10.1016/s0002-9149(96)00216-0.


The presence of an accessory hepatic vein to the pulmonary venous atrium should be considered in the setting of progressive cyanosis following the Fontan procedure. An inferior vena caval angiogram with "levo-phase" should demonstrate it. Surgical intervention or transcatheter occlusion should lead to prompt resolution of cyanosis.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Cyanosis / diagnostic imaging
  • Cyanosis / etiology*
  • Female
  • Fontan Procedure*
  • Heart Atria
  • Hepatic Veins / abnormalities*
  • Humans
  • Male
  • Postoperative Complications / diagnostic imaging
  • Postoperative Complications / etiology*
  • Pulmonary Veins / abnormalities
  • Radiography
  • Vena Cava, Inferior / diagnostic imaging