A 38-year-old man visited our hospital complaining of severe right flank pain with hematoemesis. Imaging studies including computerized tomographic (CT) scan demonstrated a right ureter stone and retroperitoneal abscess. His septic condition and presence of disseminated intravescular coagulation (DIC) necessitated percutaneous nephrostomy and drainage of the abscess. The patient recovered from DIC and infection within a week. To our knowledge, 5 similar cases of retroperitoneal abscess secondary to ureteral rupture have been reported in the Japanese literature.