The clinical features of the hereditary and nonhereditary polyposis syndromes

Surg Oncol Clin N Am. 1996 Jul;5(3):553-67.

Abstract

The polyposis syndromes are rare familial and noninherited syndromes associated with intestinal as well as extraintestinal malignancies in many cases. Their recognition and classification are critical in determining the appropriate management strategies.

Publication types

  • Review

MeSH terms

  • Adenomatous Polyposis Coli / diagnosis
  • Adenomatous Polyposis Coli / genetics
  • Adenomatous Polyposis Coli / pathology
  • Adenomatous Polyposis Coli / surgery
  • Colectomy
  • Genes, APC
  • Hamartoma Syndrome, Multiple / diagnosis
  • Hamartoma Syndrome, Multiple / pathology
  • Humans
  • Intestinal Polyps / diagnosis*
  • Intestinal Polyps / genetics
  • Intestinal Polyps / pathology
  • Intestinal Polyps / surgery
  • Peutz-Jeghers Syndrome / diagnosis