Ehlers-Danlos syndrome with a spontaneous caroticocavernous fistula occluded by detachable balloon: case report and review of literature

Neuroradiology. 1996 Aug;38(6):595-7. doi: 10.1007/BF00626107.


We report a caroticocavernous fistula (CCF) treated by an endovascular procedure in a young woman with Ehlers-Danlos syndrome type IV, with severe bilateral carotid and vertebral artery dysplasia. The CCF, which appeared after minor trauma, was successfully occluded by a detachable balloon introduced into the venous side by an arterial approach. Six previously published cases are reviewed, five successfully treated. The difficulties and risks of the endovascular procedure due to the vascular changes, are emphasised. The possibility of the venous approach is discussed.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Arteriovenous Fistula / diagnostic imaging
  • Arteriovenous Fistula / therapy*
  • Carotid Artery, Internal* / diagnostic imaging
  • Catheterization / instrumentation*
  • Cavernous Sinus* / diagnostic imaging
  • Cerebral Angiography
  • Ehlers-Danlos Syndrome / therapy*
  • Embolization, Therapeutic / instrumentation*
  • Female
  • Humans