Pulmonary hypertension developing after alglucerase therapy in two patients with type 1 Gaucher disease complicated by the hepatopulmonary syndrome

Ann Intern Med. 1996 Dec 1;125(11):901-4. doi: 10.7326/0003-4819-125-11-199612010-00005.
No abstract available

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adult
  • Dilatation, Pathologic / complications
  • Dilatation, Pathologic / drug therapy
  • Female
  • Gaucher Disease / complications
  • Gaucher Disease / drug therapy*
  • Gaucher Disease / pathology
  • Glucosylceramidase / adverse effects*
  • Hepatomegaly / complications*
  • Hepatomegaly / drug therapy
  • Humans
  • Hypertension, Pulmonary / chemically induced*
  • Hypoxia / complications*
  • Hypoxia / drug therapy
  • Male
  • Pulmonary Artery / pathology*
  • Syndrome

Substances

  • alglucerase
  • Glucosylceramidase