Cochlear implantation in children with cochlear malformations

Am J Otol. 1997 Mar;18(2):184-7.


Objective: To address the surgical and habilitative issues raised by cochlear implantation in children with cochlear dysplasia.

Study design: The English-language literature is reviewed and the New York University Medical Center experience with three patients is detailed. Two hundred institutions performing cochlear implants were queried by questionnaire.

Setting: Hospitals performing cochlear implantation.

Patients: Pediatric patients with a cochlear implant in an ear with a dysplastic cochlea.

Main outcome measures: Preoperative computed tomography analysis of cochlear anatomy was compared with operative findings, complications, and postoperative device use.

Results: Facial nerve anatomy was anomalous in 16% of patients, and there were two surgical injuries. There were no cases of meningitis. All patients who received multichannel implants derive benefit and wear their devices.

Conclusions: All degrees of cochlear dysplasia, ranging from incomplete partition to common cavity, can be safely implanted and auditory responses expected.

Publication types

  • Comparative Study

MeSH terms

  • Adult
  • Child
  • Cochlea / abnormalities*
  • Cochlea / surgery*
  • Cochlear Implants*
  • Deafness / rehabilitation
  • Facial Nerve / physiopathology
  • Female
  • Humans
  • Male
  • Surveys and Questionnaires