Congenital orbital teratoma

Aust N Z J Ophthalmol. 1997 Feb;25(1):63-6. doi: 10.1111/j.1442-9071.1997.tb01277.x.


Background: The occurrence of proptosis at birth is unusual and may be associated with a variety of tumours and structural abnormalities. Congenital orbital teratoma is a rare cause of congenital proptosis.

Methods: A case report is presented of a female infant with gross right proptosis.

Results: Computed tomography demonstrated a characteristic multicystic structure with no intracranial involvement. Histological examination found tissues derived from all three germ cell layers, consistent with a congenita orbital teratoma. The tumour was successfully removed preserving the globe and vision.

Conclusions: This report is an example of how early surgical intervention may allow preservation of the globe and vision in some patients with congenital orbital teratoma.

Publication types

  • Case Reports

MeSH terms

  • Exophthalmos / etiology
  • Female
  • Follow-Up Studies
  • Humans
  • Infant, Newborn
  • Orbital Neoplasms / congenital*
  • Orbital Neoplasms / pathology
  • Orbital Neoplasms / surgery
  • Reflex, Pupillary
  • Teratoma / congenital*
  • Teratoma / pathology
  • Teratoma / surgery
  • Tomography, X-Ray Computed