A congenitally "poor" pulmonary artery is a major reason for exclusion from Fontan operation

Heart Vessels. 1996;11(4):197-202. doi: 10.1007/BF02559992.

Abstract

We reviewed the clinical records of 185 patients who were possible candidates for Fontan operation. We did this to clarify whether all patients with suitable anomalies ultimately underwent a Fontan operation. Of the 152 patients with decreased pulmonary blood flow, 38 (26%) did not fulfill the criteria for Fontan operation, and 17 of the 33 patients (52%) with increased pulmonary blood flow (P < 0.01) were excluded as candidates. Of 48 non-candidate survivors, 19 had high pulmonary artery (PA) pressure or resistance and small PA (which we term "poor PA"), 17 had pulmonary hypertension, 6 had a markedly distorted PA, and 6 had severe ventricular dysfunction. A significant proportion of possible candidates with a suitable anomaly ultimately did not undergo a Fontan operation, because of "poor PA", a congenital condition that precluded Fontan operation.

MeSH terms

  • Adolescent
  • Adult
  • Blood Flow Velocity
  • Cardiac Catheterization / methods
  • Child
  • Child, Preschool
  • Contraindications
  • Fontan Procedure* / mortality
  • Heart Defects, Congenital / complications
  • Heart Defects, Congenital / physiopathology
  • Heart Defects, Congenital / surgery
  • Humans
  • Hypertension, Pulmonary / complications
  • Hypertension, Pulmonary / physiopathology
  • Infant
  • Palliative Care / methods
  • Pulmonary Artery / abnormalities*
  • Pulmonary Artery / physiopathology
  • Retrospective Studies
  • Survival Rate
  • Vascular Resistance