Otodental syndrome

Gen Dent. 1996 Sep-Oct;44(5):427-9.


Otodental dysplasia, a form of ectodermal dysplasia, is characterized by abnormal dental crown morphology and sensorineural hearing loss. A variety of dental abnormalities are prominent features of this syndrome--most notably gigantic, bulbous posterior teeth. In this case, a sibling is identifies in a family with otodental syndrome that had been diagnosed earlier. A unique opportunity is provided to view the intact adult dentition and possible complications for dental treatment.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Ectodermal Dysplasia / genetics
  • Ectodermal Dysplasia / pathology*
  • Family Health
  • Hearing Loss, Sensorineural / genetics
  • Humans
  • Male
  • Molar / abnormalities*
  • Syndrome
  • Tooth Abnormalities / genetics*
  • Tooth Abnormalities / pathology
  • Tooth Crown / abnormalities*