A review of literature concerning the relationship between coeliac disease and lymphoma has been done. There is a general agreement on the greater risk for development of malignant lymphoma in coeliac patients than in general population. The traditional debate around the question of whether or not T cell lymphoma may be a cause or an effect of coeliac disease to be continued. The recently results are suggestive of a protective role for a gluten-free-diet against malignancy in coeliac disease and give further support for advising all patients to adhere to a strict gluten-free-diet for life.