Susac's syndrome: a rare cause of fluctuating sensorineural hearing loss

N D Bateman; I J Johnson; K P Gibbin

doi:10.1017/s0022215100139374

Susac's syndrome: a rare cause of fluctuating sensorineural hearing loss

J Laryngol Otol. 1997 Nov;111(11):1072-4. doi: 10.1017/s0022215100139374.

Authors

N D Bateman¹, I J Johnson, K P Gibbin

Affiliation

¹ Department of Otolaryngology-Head and Neck Surgery, University Hospital, Nottingham, UK.

PMID: 9472581
DOI: 10.1017/s0022215100139374

Abstract

Susac's syndrome is extremely rare and is characterized by the clinical triad of encephalopathy, retinal artery occlusion and deafness. A case of this rare syndrome is presented and for the first time the fluctuating nature of the hearing loss is demonstrated. The site and nature of the hearing loss has been investigated. The value of neural hearing loss as a method of monitoring the clinical severity is discussed.

Publication types

Case Reports

MeSH terms

Adult
Audiometry, Pure-Tone
Brain / pathology
Central Nervous System Diseases / pathology*
Diagnosis, Differential
Female
Fundus Oculi
Hearing Loss, Sensorineural / pathology*
Humans
Magnetic Resonance Imaging
Multiple Sclerosis / diagnosis
Retinal Artery Occlusion / pathology*
Syndrome