Nevoid basal cell carcinoma syndrome in a black child

J Am Acad Dermatol. 1998 Feb;38(2 Pt 2):363-5. doi: 10.1016/s0190-9622(98)70585-7.


Nevoid basal cell carcinoma syndrome (NBCCS) is rare in black persons. We describe an 11-year-old black boy with NBCCS who presented with exotropia and a painful, expanding, cystic mass in the left posterior alveolar ridge. Further examination revealed odontogenic keratocysts with palmar and plantar pitting. Less than 5% of reported patients with NBCCS are black. To our knowledge, this is the first report of a black patient with NBCCS presenting with exotropia and an impacted molar displaced into the orbit by an odontogenic keratocyst.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Basal Cell Nevus Syndrome / diagnosis*
  • Black People*
  • Child
  • Diagnosis, Differential
  • Exotropia / diagnosis
  • Humans
  • Jaw Diseases / complications
  • Jaw Diseases / diagnosis
  • Male
  • Maxilla
  • Molar
  • Odontogenic Cysts / complications
  • Odontogenic Cysts / diagnosis
  • Orbit
  • Tooth, Impacted / complications
  • Tooth, Impacted / diagnosis