Abstract
Two siblings suffering from mental retardation, progressive bronchiectasis, extensive warts, and persistent hepatitis B are described. The propositus also had an unusual physiognomy and non-specific colitis. Both patients had a marked decrease in the population of CD4+ helper T cells.
Publication types
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Case Reports
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Research Support, Non-U.S. Gov't
MeSH terms
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Adolescent
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Bronchiectasis / etiology
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Bronchiectasis / immunology
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Colitis / complications
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Colitis / immunology
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Female
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Hepatitis B / complications
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Hepatitis B / immunology
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Humans
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Male
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T-Lymphocytopenia, Idiopathic CD4-Positive / complications
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T-Lymphocytopenia, Idiopathic CD4-Positive / genetics*
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T-Lymphocytopenia, Idiopathic CD4-Positive / immunology
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Warts / complications
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Warts / immunology