Hereditary CD4+ T lymphocytopenia

Arch Dis Child. 1998 Apr;78(4):371-2. doi: 10.1136/adc.78.4.371.

Abstract

Two siblings suffering from mental retardation, progressive bronchiectasis, extensive warts, and persistent hepatitis B are described. The propositus also had an unusual physiognomy and non-specific colitis. Both patients had a marked decrease in the population of CD4+ helper T cells.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Bronchiectasis / etiology
  • Bronchiectasis / immunology
  • Colitis / complications
  • Colitis / immunology
  • Female
  • Hepatitis B / complications
  • Hepatitis B / immunology
  • Humans
  • Male
  • T-Lymphocytopenia, Idiopathic CD4-Positive / complications
  • T-Lymphocytopenia, Idiopathic CD4-Positive / genetics*
  • T-Lymphocytopenia, Idiopathic CD4-Positive / immunology
  • Warts / complications
  • Warts / immunology