Background: Erosive adenomatosis of the nipple is a rare but distinct benign tumor of the nipple. It is usually considered to be derived from the apocrine sweat ducts of the nipple epithelium but probably of lactiferous duct origin. Total excision is the treatment of choice.
Objective: We report the clinical and histological features of this rare tumor, and the surgical technique employed.
Methods: Treatment consisted of Mohs micrographic surgery (MMS), fresh tissue technique, followed by primary closure.
Results: The described procedure resulted in a cure of the erosive adenomatosis of the nipple.
Conclusion: Total excision of erosive adenomatosis of the nipple can be obtained by MMS. This technique prevents recurrence of the disease and minimizes resulting deformation of this important anatomic area.