In utero decompression of a cystic grade IV sacrococcygeal teratoma

Fetal Diagn Ther. 1998 Sep-Oct;13(5):305-8. doi: 10.1159/000020859.

Abstract

Sacrococcygeal teratomas (SCT) are the most common congenital tumors in the newborn. The prevalence rate is approximately 1 per 40,000 births, with 80% occurring in females. The majority of these tumors are external, protruding from the perineal region. Intrapelvic SCTs, by contrast, are extremely rare and difficult to diagnose in utero. Only 15% of the SCTs are entirely cystic, the majority being mixed or solid tumors. We describe a case of a fetal cystic presacral (grade IV) SCT, discovered at 22 weeks of gestation, which resulted in bilateral ureteral obstruction and hydronephrosis. This is the first known reported case of prenatally decompressing a cystic SCT via an amniotic catheter to alleviate a mass effect in the fetus.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Decompression
  • Female
  • Fetal Diseases / therapy*
  • Gestational Age
  • Humans
  • Hydronephrosis / etiology
  • Hydronephrosis / surgery
  • Infant, Newborn
  • Pregnancy
  • Sacrococcygeal Region*
  • Teratoma / complications
  • Teratoma / diagnosis
  • Teratoma / therapy*
  • Ultrasonography, Prenatal
  • Ureteral Obstruction / etiology
  • Ureteral Obstruction / surgery