Congenital absence of the internal carotid artery

Cardiovasc Intervent Radiol. 1999 Jan;22(1):74-8. doi: 10.1007/s002709900334.


We report three cases of congenital absence of an internal carotid artery (ICA), diagnosed incidentally by digital subtraction angiography. The analysis of the cases is based on the classification of segmental ICA agenesis proposed by Lasjaunias and Berenstein. Usually the patients with this rare vascular anomaly are asymptomatic; some may have symptoms related to cerebrovascular insufficiency, compression by enlarged intracranial collateral vessels, or complications associated with cerebral aneurysms. Diagnosis of congenital absence of ICA is made by skull base computed tomography (CT) scan, CT and magnetic resonance angiography, and conventional or digital subtraction angiography.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Aged
  • Carotid Artery, Internal / abnormalities*
  • Carotid Artery, Internal / diagnostic imaging
  • Cerebrovascular Disorders / diagnosis*
  • Cerebrovascular Disorders / therapy
  • Diagnosis, Differential
  • Female
  • Humans
  • Intracranial Aneurysm / diagnosis*
  • Intracranial Aneurysm / surgery
  • Magnetic Resonance Angiography
  • Male
  • Middle Aged
  • Tomography, X-Ray Computed