Protein fate in neurodegenerative proteinopathies: polyglutamine diseases join the (mis)fold

Am J Hum Genet. 1999 Feb;64(2):339-45. doi: 10.1086/302269.
No abstract available

Publication types

  • Review

MeSH terms

  • Animals
  • Cell Nucleus / metabolism
  • Disease Progression
  • Endopeptidases / metabolism
  • Humans
  • Molecular Chaperones
  • Neurodegenerative Diseases / etiology*
  • Neurodegenerative Diseases / physiopathology
  • Peptides* / metabolism
  • Protein Folding*
  • Proteins / metabolism

Substances

  • Molecular Chaperones
  • Peptides
  • Proteins
  • polyglutamine
  • Endopeptidases