Increased RhoA pathway activation downstream of αIIbβ3/SRC contributes to heterozygous Bernard Soulier syndrome.
Lordier L, Di Buduo CA, Kauskot A, Balayn N, Lavenu-Bombled C, Baschieri F, Proulle V, Oyarzun CPM, Careddu F, Biunno I, Manoliu T, Rameau P, Plo I, Papadopoulos N, Constantinescu S, Vainchenker W, Nguyen GN, Ballerini P, Favier R, Balduini A, Raslova H.
Lordier L, et al. Among authors: baschieri f.
Haematologica. 2025 Jul 1;110(7):1596-1609. doi: 10.3324/haematol.2024.286424. Epub 2025 Mar 6.
Haematologica. 2025.
PMID: 40045897
Free PMC article.