Optimizing evaluation in pediatric and young adult patients with Marfan syndrome: Novel longitudinal metrics to track growth of aortic structures.
Bhimani SA, Rahmy A, Kim S, Jin JB, Zahka K, Komarlu R, Svensson LG, Pande A, Karamlou T; Members of Marfan Working Group; Rajeswaran J, Kalahasti V, Desai M, Roselli E, Salim-Hammoud M, Frankel WC, Pettersson G, Blackstone EH, Najm HK, Klein J.
Bhimani SA, et al.
J Thorac Cardiovasc Surg. 2022 Sep;164(3):724-740.e6. doi: 10.1016/j.jtcvs.2021.12.056. Epub 2022 Mar 16.
J Thorac Cardiovasc Surg. 2022.
PMID: 35450696
Free article.
Baseline echocardiography data were: CSA/Ht, 3.9 1.4 cm(2)/m; ARd, 2.4 0.89 cm; and ARz, 2.4 1.7. CSA/Ht tracked ARd better compared with ARz (r = 0.91 vs 0.24). ...Surgical repair occurred at CSA/Ht between 5 and 7 cm(2)/m. CONCLUSIONS: CSA/Ht tracked ARd wel …
Baseline echocardiography data were: CSA/Ht, 3.9 1.4 cm(2)/m; ARd, 2.4 0.89 cm; and ARz, 2.4 1.7. CSA/Ht tracked ARd better com …