Asymptomatic pediatric pulmonic valve myxoma involving the right ventricular outflow tract: a case report and review of the literature

J Heart Valve Dis. 2012 May;21(3):398-400.

Abstract

Asymptomatic pediatric pulmonic valve myxoma involving the right ventricular out flow tract (RVOT) is very rare. The case is presented of 13-year-old asymptomatic boy who was referred to the cardiology clinic for evaluation of murmur, and was found to have a large mobile mass (3 x 2 cm) in the RVOT that protruded into the pulmonary artery across the pulmonary valve during systole, and relocated in the right ventricle in diastole. The patient underwent successful surgical excision of the tumor, which had a short stalk attached to the pulmonary valve. Macroscopic examination revealed a typical myxoma without any evidence of malignancy. This case elaborates the importance of early recognition and surgical excision of these tumors in order to prevent thromboembolic complications.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Cardiac Surgical Procedures / methods*
  • Dissection / methods*
  • Early Medical Intervention
  • Echocardiography, Transesophageal / methods
  • Heart Murmurs / diagnosis
  • Heart Murmurs / etiology
  • Heart Murmurs / physiopathology
  • Heart Neoplasms* / complications
  • Heart Neoplasms* / pathology
  • Heart Neoplasms* / physiopathology
  • Heart Neoplasms* / surgery
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / physiopathology
  • Humans
  • Male
  • Myxoma* / complications
  • Myxoma* / pathology
  • Myxoma* / physiopathology
  • Myxoma* / surgery
  • Perioperative Care
  • Pulmonary Valve* / pathology
  • Pulmonary Valve* / physiopathology
  • Pulmonary Valve* / surgery
  • Secondary Prevention
  • Treatment Outcome