Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation

Search Page

Filters

My NCBI Filters

Text availability

Article attribute

Article type

Publication date

Search Results

359 results

Filters applied: . Clear all
Results are displayed in a computed author sort order. The Results By Year timeline is not available.
Page 1
Use of cough swabs in a cystic fibrosis clinic.
Equi AC, Pike SE, Davies J, Bush A. Equi AC, et al. Arch Dis Child. 2001 Nov;85(5):438-9. doi: 10.1136/adc.85.5.438. Arch Dis Child. 2001. PMID: 11668115 Free PMC article.
Airway surface pH in subjects with cystic fibrosis.
McShane D, Davies JC, Davies MG, Bush A, Geddes DM, Alton EW. McShane D, et al. Among authors: davies mg, davies jc. Eur Respir J. 2003 Jan;21(1):37-42. doi: 10.1183/09031936.03.00027603. Eur Respir J. 2003. PMID: 12570106 Free article.
Exploring the mechanisms of macrolides in cystic fibrosis.
Equi AC, Davies JC, Painter H, Hyde S, Bush A, Geddes DM, Alton EW. Equi AC, et al. Among authors: davies jc. Respir Med. 2006 Apr;100(4):687-97. doi: 10.1016/j.rmed.2005.07.016. Epub 2005 Sep 26. Respir Med. 2006. PMID: 16185859 Free article.
Bronchoscopy following diagnosis with cystic fibrosis.
Hilliard TN, Sukhani S, Francis J, Madden N, Rosenthal M, Balfour-Lynn I, Bush A, Davies JC. Hilliard TN, et al. Among authors: davies jc. Arch Dis Child. 2007 Oct;92(10):898-9. doi: 10.1136/adc.2006.105825. Epub 2006 Nov 6. Arch Dis Child. 2007. PMID: 17088336 Free PMC article.
Lung function from infancy to the preschool years after clinical diagnosis of cystic fibrosis.
Kozlowska WJ, Bush A, Wade A, Aurora P, Carr SB, Castle RA, Hoo AF, Lum S, Price J, Ranganathan S, Saunders C, Stanojevic S, Stroobant J, Wallis C, Stocks J; London Cystic Fibrosis Collaboration. Kozlowska WJ, et al. Am J Respir Crit Care Med. 2008 Jul 1;178(1):42-9. doi: 10.1164/rccm.200710-1599OC. Epub 2008 Apr 10. Am J Respir Crit Care Med. 2008. PMID: 18403721
Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation.
Davies JC, Wainwright CE, Canny GJ, Chilvers MA, Howenstine MS, Munck A, Mainz JG, Rodriguez S, Li H, Yen K, Ordoñez CL, Ahrens R; VX08-770-103 (ENVISION) Study Group. Davies JC, et al. Am J Respir Crit Care Med. 2013 Jun 1;187(11):1219-25. doi: 10.1164/rccm.201301-0153OC. Am J Respir Crit Care Med. 2013. PMID: 23590265 Free PMC article. Clinical Trial.
Lung clearance index: evidence for use in clinical trials in cystic fibrosis.
Kent L, Reix P, Innes JA, Zielen S, Le Bourgeois M, Braggion C, Lever S, Arets HG, Brownlee K, Bradley JM, Bayfield K, O'Neill K, Savi D, Bilton D, Lindblad A, Davies JC, Sermet I, De Boeck K; European Cystic Fibrosis Society Clinical Trial Network (ECFS-CTN) Standardisation Committee. Kent L, et al. Among authors: davies jc. J Cyst Fibros. 2014 Mar;13(2):123-38. doi: 10.1016/j.jcf.2013.09.005. Epub 2013 Dec 5. J Cyst Fibros. 2014. PMID: 24315208 Free article. Review.
Pseudomonas aeruginosa infection in cystic fibrosis: pathophysiological mechanisms and therapeutic approaches.
Lund-Palau H, Turnbull AR, Bush A, Bardin E, Cameron L, Soren O, Wierre-Gore N, Alton EW, Bundy JG, Connett G, Faust SN, Filloux A, Freemont P, Jones A, Khoo V, Morales S, Murphy R, Pabary R, Simbo A, Schelenz S, Takats Z, Webb J, Williams HD, Davies JC. Lund-Palau H, et al. Among authors: davies jc. Expert Rev Respir Med. 2016 Jun;10(6):685-97. doi: 10.1080/17476348.2016.1177460. Epub 2016 May 13. Expert Rev Respir Med. 2016. PMID: 27175979 Free article. Review.
Current and future therapies for Pseudomonas aeruginosa infection in patients with cystic fibrosis.
Smith WD, Bardin E, Cameron L, Edmondson CL, Farrant KV, Martin I, Murphy RA, Soren O, Turnbull AR, Wierre-Gore N, Alton EW, Bundy JG, Bush A, Connett GJ, Faust SN, Filloux A, Freemont PS, Jones AL, Takats Z, Webb JS, Williams HD, Davies JC. Smith WD, et al. Among authors: davies jc. FEMS Microbiol Lett. 2017 Aug 1;364(14). doi: 10.1093/femsle/fnx121. FEMS Microbiol Lett. 2017. PMID: 28854668 Review.
Pooling of bronchoalveolar lavage in children with cystic fibrosis does not adversely affect the microbiological yield or sensitivity in detecting pulmonary inflammation.
McNally P, O'Rourke J, Fantino E, Chacko A, Pabary R, Turnbull A, Grant T, O'Sullivan N, Wainwright C, Linnane B, Davies JC, Sly PD. McNally P, et al. Among authors: davies jc. J Cyst Fibros. 2018 May;17(3):391-399. doi: 10.1016/j.jcf.2017.10.016. Epub 2017 Nov 20. J Cyst Fibros. 2018. PMID: 29157921 Free article.
Outdoor air pollution and cystic fibrosis.
Brugha R, Edmondson C, Davies JC. Brugha R, et al. Among authors: davies jc. Paediatr Respir Rev. 2018 Sep;28:80-86. doi: 10.1016/j.prrv.2018.03.005. Epub 2018 Apr 11. Paediatr Respir Rev. 2018. PMID: 29793860
Inconclusive diagnosis after a positive newborn bloodspot screening result for cystic fibrosis; clarification of the harmonised international definition.
Southern KW, Barben J, Gartner S, Munck A, Castellani C, Mayell SJ, Davies JC, Winters V, Murphy J, Salinas D, McColley SA, Ren CL, Farrell PM. Southern KW, et al. Among authors: davies jc. J Cyst Fibros. 2019 Nov;18(6):778-780. doi: 10.1016/j.jcf.2019.04.010. Epub 2019 Apr 24. J Cyst Fibros. 2019. PMID: 31027826 Free article. No abstract available.
An open-label extension study of ivacaftor in children with CF and a CFTR gating mutation initiating treatment at age 2-5 years (KLIMB).
Rosenfeld M, Cunningham S, Harris WT, Lapey A, Regelmann WE, Sawicki GS, Southern KW, Chilvers M, Higgins M, Tian S, Cooke J, Davies JC; KLIMB study group. Rosenfeld M, et al. Among authors: davies jc. J Cyst Fibros. 2019 Nov;18(6):838-843. doi: 10.1016/j.jcf.2019.03.009. Epub 2019 Apr 30. J Cyst Fibros. 2019. PMID: 31053538 Free PMC article. Clinical Trial.
Abnormal pro-gly-pro pathway and airway neutrophilia in pediatric cystic fibrosis.
Turnbull AR, Pyle CJ, Patel DF, Jackson PL, Hilliard TN, Regamey N, Tan HL, Brown S, Thursfield R, Short C, Mc Fie M, Alton EWFW, Gaggar A, Blalock JE, Lloyd CM, Bush A, Davies JC, Snelgrove RJ. Turnbull AR, et al. Among authors: davies jc. J Cyst Fibros. 2020 Jan;19(1):40-48. doi: 10.1016/j.jcf.2019.05.017. Epub 2019 Jun 5. J Cyst Fibros. 2020. PMID: 31176670 Free PMC article.
Speeding up access to new drugs for CF: Considerations for clinical trial design and delivery.
Davies JC, Drevinek P, Elborn JS, Kerem E, Lee T; European CF Society (ECFS) Strategic Planning Task Force on ‘Speeding up access to new 4 drugs for CF’; Amaral MD, de Boeck K, Davies JC, Drevinek P, Elborn JS, Kerem E, Lee T. Davies JC, et al. J Cyst Fibros. 2019 Sep;18(5):677-684. doi: 10.1016/j.jcf.2019.06.011. Epub 2019 Jul 11. J Cyst Fibros. 2019. PMID: 31303382 Free article.
Fair selection of participants in clinical trials: The challenge to push the envelope further.
Davies JC, Scott S, Dobra R, Brendell R, Brownlee K, Carr SB, Cosgriff R, Simmonds NJ; London Network of Clinical Trials Accelerator Platform sites; Jahan R, Jones A, Matthews J, Brown S, Galono K, Miles K, Pao C, Shafi N, Watson D, Orchard C, Davies G, Pike K, Shah S, Bossley CJ, Fong T, Macedo P, Ruiz G, Waller M, Baker L. Davies JC, et al. Among authors: davies g. J Cyst Fibros. 2019 Sep;18(5):e48-e50. doi: 10.1016/j.jcf.2019.07.004. Epub 2019 Aug 9. J Cyst Fibros. 2019. PMID: 31405729 Free article. No abstract available.
'Go for it, dream big, work hard and persist': A message to the next generation of CF leaders in recognition of International Women's Day 2020.
Langawi MA, Byrnes C, Davies JC, Hamouda S, Kabra M, Rached SZ, Sands D, Shteinberg M, Taylor-Cousar J, Tullis E, Wainwright C. Langawi MA, et al. Among authors: davies jc. J Cyst Fibros. 2020 Mar;19(2):184-193. doi: 10.1016/j.jcf.2020.02.021. Epub 2020 Mar 7. J Cyst Fibros. 2020. PMID: 32156627 Free article. Review.
Building global development strategies for cf therapeutics during a transitional cftr modulator era.
Mayer-Hamblett N, van Koningsbruggen-Rietschel S, Nichols DP, VanDevanter DR, Davies JC, Lee T, Durmowicz AG, Ratjen F, Konstan MW, Pearson K, Bell SC, Clancy JP, Taylor-Cousar JL, De Boeck K, Donaldson SH, Downey DG, Flume PA, Drevinek P, Goss CH, Fajac I, Magaret AS, Quon BS, Singleton SM, VanDalfsen JM, Retsch-Bogart GZ. Mayer-Hamblett N, et al. Among authors: davies jc. J Cyst Fibros. 2020 Sep;19(5):677-687. doi: 10.1016/j.jcf.2020.05.011. Epub 2020 Jun 7. J Cyst Fibros. 2020. PMID: 32522463 Free PMC article. Review.
Monitoring early stage lung disease in cystic fibrosis.
Nissenbaum C, Davies G, Horsley A, Davies JC. Nissenbaum C, et al. Among authors: davies g, davies jc. Curr Opin Pulm Med. 2020 Nov;26(6):671-678. doi: 10.1097/MCP.0000000000000732. Curr Opin Pulm Med. 2020. PMID: 32925367 Review.
A phase 3, double-blind, parallel-group study to evaluate the efficacy and safety of tezacaftor in combination with ivacaftor in participants 6 through 11 years of age with cystic fibrosis homozygous for F508del or heterozygous for the F508del-CFTR mutation and a residual function mutation.
Davies JC, Sermet-Gaudelus I, Naehrlich L, Harris RS, Campbell D, Ahluwalia N, Short C, Haseltine E, Panorchan P, Saunders C, Owen CA, Wainwright CE; VX16-661-115 Investigator Group. Davies JC, et al. J Cyst Fibros. 2021 Jan;20(1):68-77. doi: 10.1016/j.jcf.2020.07.023. Epub 2020 Sep 21. J Cyst Fibros. 2021. PMID: 32967799 Free article. Clinical Trial.
Updated guidance on the management of children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID).
Barben J, Castellani C, Munck A, Davies JC, de Winter-de Groot KM, Gartner S, Kashirskaya N, Linnane B, Mayell SJ, McColley S, Ooi CY, Proesmans M, Ren CL, Salinas D, Sands D, Sermet-Gaudelus I, Sommerburg O, Southern KW; European CF Society Neonatal Screening Working Group (ECFS NSWG). Barben J, et al. Among authors: davies jc. J Cyst Fibros. 2021 Sep;20(5):810-819. doi: 10.1016/j.jcf.2020.11.006. Epub 2020 Nov 27. J Cyst Fibros. 2021. PMID: 33257262 Free article. Review.
Optimising equity of access: how should we allocate slots to the most competitive trials in Cystic Fibrosis (CF)?
Dobra R, Davies G, Pike K, Strassle C, Allen L, Brendell R, Brownlee K, Carr SB, Simmonds NJ, Davies JC; London Network of Clinical Trials Accelerator Platform sites and affiliates. Dobra R, et al. Among authors: davies g, davies jc. J Cyst Fibros. 2021 Nov;20(6):978-985. doi: 10.1016/j.jcf.2021.03.027. Epub 2021 Apr 17. J Cyst Fibros. 2021. PMID: 33875366 Free article.
Targeted exhaled breath analysis for detection of Pseudomonas aeruginosa in cystic fibrosis patients.
Kos R, Brinkman P, Neerincx AH, Paff T, Gerritsen MG, Lammers A, Kraneveld AD, Heijerman HGM, Janssens HM, Davies JC, Majoor CJ, Weersink EJ, Sterk PJ, Haarman EG, Bos LD, Maitland-van der Zee AH; Amsterdam Mucociliary Clearance Disease (AMCD) Research Group and the Amsterdam UMC Breath Research Group. Kos R, et al. Among authors: davies jc. J Cyst Fibros. 2022 Jan;21(1):e28-e34. doi: 10.1016/j.jcf.2021.04.015. Epub 2021 May 18. J Cyst Fibros. 2022. PMID: 34016557 Free article. Review.
Cystic fibrosis.
Shteinberg M, Haq IJ, Polineni D, Davies JC. Shteinberg M, et al. Among authors: davies jc. Lancet. 2021 Jun 5;397(10290):2195-2211. doi: 10.1016/S0140-6736(20)32542-3. Lancet. 2021. PMID: 34090606 Review.
Telemedicine and cystic fibrosis: Do we still need face-to-face clinics?
Dixon E, Dick K, Ollosson S, Jones D, Mattock H, Bentley S, Saunders C, Matthews J, Dobra B, King J, Edmondson C, Davies JC. Dixon E, et al. Among authors: davies jc. Paediatr Respir Rev. 2022 Jun;42:23-28. doi: 10.1016/j.prrv.2021.05.002. Epub 2021 May 19. Paediatr Respir Rev. 2022. PMID: 34215541 Review.
Riociguat for the treatment of Phe508del homozygous adults with cystic fibrosis.
Derichs N, Taylor-Cousar JL, Davies JC, Fajac I, Tullis E, Nazareth D, Downey DG, Rosenbluth D, Malfroot A, Saunders C, Jensen R, Solomon GM, Vermeulen F, Kaiser A, Willmann S, Saleh S, Droebner K, Sandner P, Bear CE, Hoffmann A, Ratjen F, Rowe SM; Rio-CF Study Group. Derichs N, et al. Among authors: davies jc. J Cyst Fibros. 2021 Nov;20(6):1018-1025. doi: 10.1016/j.jcf.2021.07.015. Epub 2021 Aug 19. J Cyst Fibros. 2021. PMID: 34419414 Free article. Clinical Trial.
The feasibility of home monitoring of young people with cystic fibrosis: Results from CLIMB-CF.
Edmondson C, Westrupp N, Seddon P, Olden C, Wallis C, Dawson C, Brodlie M, Baxter F, McCormick J, MacFarlane S, Rice D, Macleod A, Brooker R, Connon M, Ghayyda S, Blaikie L, Thursfield R, Brown L, Price A, Fleischer E, Itterman J, Hughes D, Barrett P, Surette M, Donnelly C, Mateos-Corral D, Padley G, Wallenburg J, Brownlee K, Alton EWFW, Bush A, Davies JC. Edmondson C, et al. Among authors: davies jc. J Cyst Fibros. 2022 Jan;21(1):70-77. doi: 10.1016/j.jcf.2021.09.018. Epub 2021 Oct 8. J Cyst Fibros. 2022. PMID: 34635459 Free article.
A Phase 3, open-label, 96-week trial to study the safety, tolerability, and efficacy of tezacaftor/ivacaftor in children ≥ 6 years of age homozygous for F508del or heterozygous for F508del and a residual function CFTR variant.
Sawicki GS, Chilvers M, McNamara J, Naehrlich L, Saunders C, Sermet-Gaudelus I, Wainwright CE, Ahluwalia N, Campbell D, Harris RS, Paz-Diaz H, Shih JL, Davies JC. Sawicki GS, et al. Among authors: davies jc. J Cyst Fibros. 2022 Jul;21(4):675-683. doi: 10.1016/j.jcf.2022.02.003. Epub 2022 Feb 18. J Cyst Fibros. 2022. PMID: 35190292 Free article. Clinical Trial.
An Update on CFTR Modulators as New Therapies for Cystic Fibrosis.
King JA, Nichols AL, Bentley S, Carr SB, Davies JC. King JA, et al. Among authors: davies jc. Paediatr Drugs. 2022 Jul;24(4):321-333. doi: 10.1007/s40272-022-00509-y. Epub 2022 May 16. Paediatr Drugs. 2022. PMID: 35570261 Review.
Pseudomonas aeruginosa in the Cystic Fibrosis Lung.
King J, Murphy R, Davies JC. King J, et al. Among authors: davies jc. Adv Exp Med Biol. 2022;1386:347-369. doi: 10.1007/978-3-031-08491-1_13. Adv Exp Med Biol. 2022. PMID: 36258079
Future therapies for cystic fibrosis.
Allen L, Allen L, Carr SB, Davies G, Downey D, Egan M, Forton JT, Gray R, Haworth C, Horsley A, Smyth AR, Southern KW, Davies JC. Allen L, et al. Among authors: davies g, davies jc. Nat Commun. 2023 Feb 8;14(1):693. doi: 10.1038/s41467-023-36244-2. Nat Commun. 2023. PMID: 36755044 Free PMC article. Review.
Standards of care for CFTR variant-specific therapy (including modulators) for people with cystic fibrosis.
Southern KW, Castellani C, Lammertyn E, Smyth A, VanDevanter D, van Koningsbruggen-Rietschel S, Barben J, Bevan A, Brokaar E, Collins S, Connett GJ, Daniels TWV, Davies J, Declercq D, Gartner S, Gramegna A, Hamilton N, Hauser J, Kashirskaya N, Kessler L, Lowdon J, Makukh H, Martin C, Morrison L, Nazareth D, Noordhoek J, O'Neill C, Owen E, Oxley H, Raraigh KS, Raynal C, Robinson K, Roehmel J, Schwarz C, Sermet I, Shteinberg M, Sinha I, Takawira C, van Mourik P, Verkleij M, Waller MD, Duff A. Southern KW, et al. J Cyst Fibros. 2023 Jan;22(1):17-30. doi: 10.1016/j.jcf.2022.10.002. Epub 2022 Oct 28. J Cyst Fibros. 2023. PMID: 36916675 Free article.
Chronic rhinosinusitis in the era of CFTR modulator therapy.
Stone RG, Short C, Davies JC, McNally P. Stone RG, et al. Among authors: davies jc. J Cyst Fibros. 2023 Sep 8:S1569-1993(23)00877-9. doi: 10.1016/j.jcf.2023.08.009. Online ahead of print. J Cyst Fibros. 2023. PMID: 37690973 Free article. Review.
Standards for the care of people with cystic fibrosis (CF).
Southern KW, Burgel PR, Castellani C, De Boeck K, Davies JC, Dunlevy F, Fajac I, Gramegna A, Lammertyn E, Middleton PG, Ratjen F, van Koningsbruggen-Rietschel S. Southern KW, et al. Among authors: davies jc. J Cyst Fibros. 2023 Nov;22(6):961-962. doi: 10.1016/j.jcf.2023.09.009. Epub 2023 Oct 3. J Cyst Fibros. 2023. PMID: 37798158 No abstract available.
The clinical use of rhDNAse.
Davies J, Trindale M, Wallis C, Rosenthal M, Bush A. Davies J, et al. Pediatr Pulmonol Suppl. 1997;16:273-4. doi: 10.1002/ppul.19502308141. Pediatr Pulmonol Suppl. 1997. PMID: 9443309 Review. No abstract available.
Prospects for gene therapy for cystic fibrosis.
Davies JC, Geddes DM, Alton EW. Davies JC, et al. Mol Med Today. 1998 Jul;4(7):292-9. doi: 10.1016/s1357-4310(98)01265-9. Mol Med Today. 1998. PMID: 9743990 Review.
Gene therapy for cystic fibrosis.
Davies JC, Geddes DM, Alton EW. Davies JC, et al. J Gene Med. 2001 Sep-Oct;3(5):409-17. doi: 10.1002/jgm.200. J Gene Med. 2001. PMID: 11601754 Review.
Modifier genes in cystic fibrosis.
Davies JC. Davies JC. Pediatr Pulmonol Suppl. 2004;26:86-7. doi: 10.1002/ppul.70062. Pediatr Pulmonol Suppl. 2004. PMID: 15029608 Review. No abstract available.
Modifier genes in cystic fibrosis.
Davies JC, Griesenbach U, Alton E. Davies JC, et al. Pediatr Pulmonol. 2005 May;39(5):383-91. doi: 10.1002/ppul.20198. Pediatr Pulmonol. 2005. PMID: 15765543 Review.
359 results