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Page 1
Rectal Organoids Enable Personalized Treatment of Cystic Fibrosis.
Berkers G, van Mourik P, Vonk AM, Kruisselbrink E, Dekkers JF, de Winter-de Groot KM, Arets HGM, Marck-van der Wilt REP, Dijkema JS, Vanderschuren MM, Houwen RHJ, Heijerman HGM, van de Graaf EA, Elias SG, Majoor CJ, Koppelman GH, Roukema J, Bakker M, Janssens HM, van der Meer R, Vries RGJ, Clevers HC, de Jonge HR, Beekman JM, van der Ent CK. Berkers G, et al. Among authors: van de graaf ea, van mourik p, van der meer r, van der ent ck. Cell Rep. 2019 Feb 12;26(7):1701-1708.e3. doi: 10.1016/j.celrep.2019.01.068. Cell Rep. 2019. PMID: 30759382 Free article.
Treatment of children with cystic fibrosis: central, local or both?
van Koolwijk LM, Uiterwaal CS, van der Laag J, Hoekstra JH, Gulmans VA, van der Ent CK. van Koolwijk LM, et al. Among authors: van der laag j, van der ent ck. Acta Paediatr. 2002;91(9):972-7; discussion 894-5. doi: 10.1080/080352502760272687. Acta Paediatr. 2002. PMID: 12412875
Impulse oscillometry: a measure for airway obstruction.
Vink GR, Arets HG, van der Laag J, van der Ent CK. Vink GR, et al. Among authors: van der laag j, van der ent ck. Pediatr Pulmonol. 2003 Mar;35(3):214-9. doi: 10.1002/ppul.10235. Pediatr Pulmonol. 2003. PMID: 12567390
Anaerobic exercise in pediatric cystic fibrosis.
Klijn PH, Terheggen-Lagro SW, Van Der Ent CK, Van Der Net J, Kimpen JL, Helders PJ. Klijn PH, et al. Among authors: van der net j, van der ent ck. Pediatr Pulmonol. 2003 Sep;36(3):223-9. doi: 10.1002/ppul.10337. Pediatr Pulmonol. 2003. PMID: 12910584
Thoracic excursion measurement in children with cystic fibrosis.
Custers JW, Arets HG, Engelbert RH, Kooijmans FT, van der Ent CK, Helders PJ. Custers JW, et al. Among authors: van der ent ck. J Cyst Fibros. 2005 May;4(2):129-33. doi: 10.1016/j.jcf.2004.12.007. J Cyst Fibros. 2005. PMID: 15914097 Free article.
Nitric oxide in cystic fibrosis.
de Winter-de Groot KM, van der Ent CK. de Winter-de Groot KM, et al. Among authors: van der ent ck. J Cyst Fibros. 2005 Aug;4 Suppl 2:25-9. doi: 10.1016/j.jcf.2005.05.008. J Cyst Fibros. 2005. PMID: 15982933 Free article. Review.
Disease modifying genes in cystic fibrosis.
Slieker MG, Sanders EA, Rijkers GT, Ruven HJ, van der Ent CK. Slieker MG, et al. Among authors: van der ent ck. J Cyst Fibros. 2005 Aug;4 Suppl 2:7-13. doi: 10.1016/j.jcf.2005.05.006. J Cyst Fibros. 2005. PMID: 15996905 Free article. Review.
Outcome of assisted ventilation for acute respiratory failure in cystic fibrosis.
Slieker MG, van Gestel JP, Heijerman HG, Tramper-Stranders GA, van Berkhout FT, van der Ent CK, Jansen NJ. Slieker MG, et al. Among authors: van gestel jp, van berkhout ft, van der ent ck. Intensive Care Med. 2006 May;32(5):754-8. doi: 10.1007/s00134-006-0085-x. Epub 2006 Mar 2. Intensive Care Med. 2006. PMID: 16518642
Pulmonary prognosis in cystic fibrosis patients with liver disease.
Slieker MG, van der Doef HP, Deckers-Kocken JM, van der Ent CK, Houwen RH. Slieker MG, et al. Among authors: van der doef hp, van der ent ck. J Pediatr. 2006 Jul;149(1):144; author reply 144-5. doi: 10.1016/j.jpeds.2005.12.018. J Pediatr. 2006. PMID: 16860146 No abstract available.
Clinical impact of a highly prevalent Pseudomonas aeruginosa clone in Dutch cystic fibrosis patients.
de Vrankrijker AM, Brimicombe RW, Wolfs TF, Heijerman HG, van Mansfeld R, van Berkhout FT, Willems RJ, Bonten MJ, van der Ent CK. de Vrankrijker AM, et al. Among authors: van mansfeld r, van berkhout ft, van der ent ck. Clin Microbiol Infect. 2011 Mar;17(3):382-5. doi: 10.1111/j.1469-0691.2010.03295.x. Epub 2010 Aug 30. Clin Microbiol Infect. 2011. PMID: 20807225 Free article.
Challenging and emerging pathogens in cystic fibrosis.
de Vrankrijker AM, Wolfs TF, van der Ent CK. de Vrankrijker AM, et al. Among authors: van der ent ck. Paediatr Respir Rev. 2010 Dec;11(4):246-54. doi: 10.1016/j.prrv.2010.07.003. Epub 2010 Aug 7. Paediatr Respir Rev. 2010. PMID: 21109184 Review.
Chronic infection and inflammation affect exercise capacity in cystic fibrosis.
van de Weert-van Leeuwen PB, Slieker MG, Hulzebos HJ, Kruitwagen CL, van der Ent CK, Arets HG. van de Weert-van Leeuwen PB, et al. Among authors: van der ent ck. Eur Respir J. 2012 Apr;39(4):893-8. doi: 10.1183/09031936.00086211. Epub 2011 Sep 1. Eur Respir J. 2012. PMID: 21885387 Free article.
PPARγ as a therapeutic target in cystic fibrosis.
Dekkers JF, van der Ent CK, Kalkhoven E, Beekman JM. Dekkers JF, et al. Among authors: van der ent ck. Trends Mol Med. 2012 May;18(5):283-91. doi: 10.1016/j.molmed.2012.03.004. Epub 2012 Apr 9. Trends Mol Med. 2012. PMID: 22494945 Review.
CFTR-mutation specific applications of CFTR-directed monoclonal antibodies.
van Meegen MA, Terheggen SW, Koymans KJ, Vijftigschild LA, Dekkers JF, van der Ent CK, Beekman JM. van Meegen MA, et al. Among authors: van der ent ck. J Cyst Fibros. 2013 Sep;12(5):487-96. doi: 10.1016/j.jcf.2012.12.005. Epub 2013 Jan 11. J Cyst Fibros. 2013. PMID: 23317763 Free article.
Optimal complement-mediated phagocytosis of Pseudomonas aeruginosa by monocytes is cystic fibrosis transmembrane conductance regulator-dependent.
Van de Weert-van Leeuwen PB, Van Meegen MA, Speirs JJ, Pals DJ, Rooijakkers SH, Van der Ent CK, Terheggen-Lagro SW, Arets HG, Beekman JM. Van de Weert-van Leeuwen PB, et al. Among authors: van der ent ck, van meegen ma. Am J Respir Cell Mol Biol. 2013 Sep;49(3):463-70. doi: 10.1165/rcmb.2012-0502OC. Am J Respir Cell Mol Biol. 2013. PMID: 23617438
A functional CFTR assay using primary cystic fibrosis intestinal organoids.
Dekkers JF, Wiegerinck CL, de Jonge HR, Bronsveld I, Janssens HM, de Winter-de Groot KM, Brandsma AM, de Jong NW, Bijvelds MJ, Scholte BJ, Nieuwenhuis EE, van den Brink S, Clevers H, van der Ent CK, Middendorp S, Beekman JM. Dekkers JF, et al. Among authors: van den brink s, van der ent ck. Nat Med. 2013 Jul;19(7):939-45. doi: 10.1038/nm.3201. Epub 2013 Jun 2. Nat Med. 2013. PMID: 23727931
Effect of long-term voluntary exercise wheel running on susceptibility to bacterial pulmonary infections in a mouse model.
van de Weert-van Leeuwen PB, de Vrankrijker AM, Fentz J, Ciofu O, Wojtaszewski JF, Arets HG, Hulzebos HJ, van der Ent CK, Beekman JM, Johansen HK. van de Weert-van Leeuwen PB, et al. Among authors: van der ent ck. PLoS One. 2013 Dec 23;8(12):e82869. doi: 10.1371/journal.pone.0082869. eCollection 2013. PLoS One. 2013. PMID: 24376599 Free PMC article.
Prediction of mortality in adolescents with cystic fibrosis.
Hulzebos EH, Bomhof-Roordink H, van de Weert-van Leeuwen PB, Twisk JW, Arets HG, van der Ent CK, Takken T. Hulzebos EH, et al. Among authors: van de weert van leeuwen pb, van der ent ck. Med Sci Sports Exerc. 2014 Nov;46(11):2047-52. doi: 10.1249/MSS.0000000000000344. Med Sci Sports Exerc. 2014. PMID: 24848493
A bioassay using intestinal organoids to measure CFTR modulators in human plasma.
Dekkers R, Vijftigschild LA, Vonk AM, Kruisselbrink E, de Winter-de Groot KM, Janssens HM, van der Ent CK, Beekman JM. Dekkers R, et al. Among authors: van der ent ck. J Cyst Fibros. 2015 Mar;14(2):178-81. doi: 10.1016/j.jcf.2014.10.007. Epub 2014 Nov 6. J Cyst Fibros. 2015. PMID: 25467948 Free article.
Development of the Nasopharyngeal Microbiota in Infants with Cystic Fibrosis.
Prevaes SM, de Winter-de Groot KM, Janssens HM, de Steenhuijsen Piters WA, Tramper-Stranders GA, Wyllie AL, Hasrat R, Tiddens HA, van Westreenen M, van der Ent CK, Sanders EA, Bogaert D. Prevaes SM, et al. Among authors: van westreenen m, van der ent ck. Am J Respir Crit Care Med. 2016 Mar 1;193(5):504-15. doi: 10.1164/rccm.201509-1759OC. Am J Respir Crit Care Med. 2016. PMID: 26492486
Potentiator synergy in rectal organoids carrying S1251N, G551D, or F508del CFTR mutations.
Dekkers JF, Van Mourik P, Vonk AM, Kruisselbrink E, Berkers G, de Winter-de Groot KM, Janssens HM, Bronsveld I, van der Ent CK, de Jonge HR, Beekman JM. Dekkers JF, et al. Among authors: van mourik p, van der ent ck. J Cyst Fibros. 2016 Sep;15(5):568-78. doi: 10.1016/j.jcf.2016.04.007. Epub 2016 May 5. J Cyst Fibros. 2016. PMID: 27160424 Free article.
The Effect of Strict Segregation on Pseudomonas aeruginosa in Cystic Fibrosis Patients.
van Mansfeld R, de Vrankrijker A, Brimicombe R, Heijerman H, Teding van Berkhout F, Spitoni C, Grave S, van der Ent C, Wolfs T, Willems R, Bonten M. van Mansfeld R, et al. PLoS One. 2016 Jun 9;11(6):e0157189. doi: 10.1371/journal.pone.0157189. eCollection 2016. PLoS One. 2016. PMID: 27280467 Free PMC article. Clinical Trial.
Characterizing responses to CFTR-modulating drugs using rectal organoids derived from subjects with cystic fibrosis.
Dekkers JF, Berkers G, Kruisselbrink E, Vonk A, de Jonge HR, Janssens HM, Bronsveld I, van de Graaf EA, Nieuwenhuis EE, Houwen RH, Vleggaar FP, Escher JC, de Rijke YB, Majoor CJ, Heijerman HG, de Winter-de Groot KM, Clevers H, van der Ent CK, Beekman JM. Dekkers JF, et al. Among authors: van de graaf ea, van der ent ck. Sci Transl Med. 2016 Jun 22;8(344):344ra84. doi: 10.1126/scitranslmed.aad8278. Sci Transl Med. 2016. PMID: 27334259
β2-Adrenergic receptor agonists activate CFTR in intestinal organoids and subjects with cystic fibrosis.
Vijftigschild LA, Berkers G, Dekkers JF, Zomer-van Ommen DD, Matthes E, Kruisselbrink E, Vonk A, Hensen CE, Heida-Michel S, Geerdink M, Janssens HM, van de Graaf EA, Bronsveld I, de Winter-de Groot KM, Majoor CJ, Heijerman HG, de Jonge HR, Hanrahan JW, van der Ent CK, Beekman JM. Vijftigschild LA, et al. Among authors: van de graaf ea, van der ent ck. Eur Respir J. 2016 Sep;48(3):768-79. doi: 10.1183/13993003.01661-2015. Epub 2016 Jul 28. Eur Respir J. 2016. PMID: 27471203 Free article. Clinical Trial.
Concordance between upper and lower airway microbiota in infants with cystic fibrosis.
Prevaes SM, de Steenhuijsen Piters WA, de Winter-de Groot KM, Janssens HM, Tramper-Stranders GA, Chu ML, Tiddens HA, van Westreenen M, van der Ent CK, Sanders EA, Bogaert D. Prevaes SM, et al. Among authors: van westreenen m, van der ent ck. Eur Respir J. 2017 Mar 29;49(3):1602235. doi: 10.1183/13993003.02235-2016. Print 2017 Mar. Eur Respir J. 2017. PMID: 28356374 Free article.
The association between a genetic risk score for allergy and the risk of developing allergies in childhood-Results of the WHISTLER cohort.
Arabkhazaeli A, Ahmadizar F, Leusink M, Arets HGM, Raaijmakers JAM, Uiterwaal CSPM, van der Ent CK, Maitland-van der Zee AH, Vijverberg SJH. Arabkhazaeli A, et al. Among authors: van der ent ck. Pediatr Allergy Immunol. 2018 Feb;29(1):72-77. doi: 10.1111/pai.12824. Epub 2017 Nov 22. Pediatr Allergy Immunol. 2018. PMID: 29047167
Stratifying infants with cystic fibrosis for disease severity using intestinal organoid swelling as a biomarker of CFTR function.
de Winter-de Groot KM, Janssens HM, van Uum RT, Dekkers JF, Berkers G, Vonk A, Kruisselbrink E, Oppelaar H, Vries R, Clevers H, Houwen RHJ, Escher JC, Elias SG, de Jonge HR, de Rijke YB, Tiddens HAWM, van der Ent CK, Beekman JM. de Winter-de Groot KM, et al. Among authors: van uum rt, van der ent ck. Eur Respir J. 2018 Sep 17;52(3):1702529. doi: 10.1183/13993003.02529-2017. Print 2018 Sep. Eur Respir J. 2018. PMID: 30166324 Free article.
Long-term expanding human airway organoids for disease modeling.
Sachs N, Papaspyropoulos A, Zomer-van Ommen DD, Heo I, Böttinger L, Klay D, Weeber F, Huelsz-Prince G, Iakobachvili N, Amatngalim GD, de Ligt J, van Hoeck A, Proost N, Viveen MC, Lyubimova A, Teeven L, Derakhshan S, Korving J, Begthel H, Dekkers JF, Kumawat K, Ramos E, van Oosterhout MF, Offerhaus GJ, Wiener DJ, Olimpio EP, Dijkstra KK, Smit EF, van der Linden M, Jaksani S, van de Ven M, Jonkers J, Rios AC, Voest EE, van Moorsel CH, van der Ent CK, Cuppen E, van Oudenaarden A, Coenjaerts FE, Meyaard L, Bont LJ, Peters PJ, Tans SJ, van Zon JS, Boj SF, Vries RG, Beekman JM, Clevers H. Sachs N, et al. Among authors: van de ven m, van hoeck a, van oosterhout mf, van zon js, van der linden m, van oudenaarden a, van moorsel ch, van der ent ck. EMBO J. 2019 Feb 15;38(4):e100300. doi: 10.15252/embj.2018100300. Epub 2019 Jan 14. EMBO J. 2019. PMID: 30643021 Free PMC article.
Intestinal organoids to model cystic fibrosis.
van Mourik P, Beekman JM, van der Ent CK. van Mourik P, et al. Among authors: van der ent ck. Eur Respir J. 2019 Jul 4;54(1):1802379. doi: 10.1183/13993003.02379-2018. Print 2019 Jul. Eur Respir J. 2019. PMID: 31023844 Free article. No abstract available.
Forskolin-induced swelling of intestinal organoids correlates with disease severity in adults with cystic fibrosis and homozygous F508del mutations.
de Winter-de Groot KM, Berkers G, Marck-van der Wilt REP, van der Meer R, Vonk A, Dekkers JF, Geerdink M, Michel S, Kruisselbrink E, Vries R, Clevers H, Vleggaar FP, Elias SG, Heijerman HGM, van der Ent CK, Beekman JM. de Winter-de Groot KM, et al. Among authors: van der meer r, van der ent ck. J Cyst Fibros. 2020 Jul;19(4):614-619. doi: 10.1016/j.jcf.2019.10.022. Epub 2019 Nov 15. J Cyst Fibros. 2020. PMID: 31735562 Free article.
Clinical effect of lumacaftor/ivacaftor in F508del homozygous CF patients with FEV1 ≥ 90% predicted at baseline.
Aalbers BL, de Winter-de Groot KM, Arets HGM, Hofland RW, de Kiviet AC, van Oirschot-van de Ven MMM, Kruijswijk MA, Schotman S, Michel S, van der Ent CK, Heijerman HGM. Aalbers BL, et al. Among authors: van oirschot van de ven mmm, van der ent ck. J Cyst Fibros. 2020 Jul;19(4):654-658. doi: 10.1016/j.jcf.2019.12.015. Epub 2020 Jan 7. J Cyst Fibros. 2020. PMID: 31924546 Free article.
CRISPR-Based Adenine Editors Correct Nonsense Mutations in a Cystic Fibrosis Organoid Biobank.
Geurts MH, de Poel E, Amatngalim GD, Oka R, Meijers FM, Kruisselbrink E, van Mourik P, Berkers G, de Winter-de Groot KM, Michel S, Muilwijk D, Aalbers BL, Mullenders J, Boj SF, Suen SWF, Brunsveld JE, Janssens HM, Mall MA, Graeber SY, van Boxtel R, van der Ent CK, Beekman JM, Clevers H. Geurts MH, et al. Among authors: van mourik p, van boxtel r, van der ent ck. Cell Stem Cell. 2020 Apr 2;26(4):503-510.e7. doi: 10.1016/j.stem.2020.01.019. Epub 2020 Feb 20. Cell Stem Cell. 2020. PMID: 32084388 Free article.
Females with cystic fibrosis have a larger decrease in sweat chloride in response to lumacaftor/ivacaftor compared to males.
Aalbers BL, Hofland RW, Bronsveld I, de Winter-de Groot KM, Arets HGM, de Kiviet AC, van Oirschot-van de Ven MMM, Kruijswijk MA, Schotman S, Michel S, van der Ent CK, Heijerman HGM. Aalbers BL, et al. Among authors: van oirschot van de ven mmm, van der ent ck. J Cyst Fibros. 2021 Jan;20(1):e7-e11. doi: 10.1016/j.jcf.2020.05.004. Epub 2020 May 21. J Cyst Fibros. 2021. PMID: 32448708 Free article.
Development of the gut microbiota in early life: The impact of cystic fibrosis and antibiotic treatment.
Kristensen M, Prevaes SMPJ, Kalkman G, Tramper-Stranders GA, Hasrat R, de Winter-de Groot KM, Janssens HM, Tiddens HA, van Westreenen M, Sanders EAM, Arets B, Keijser B, van der Ent CK, Bogaert D. Kristensen M, et al. Among authors: van westreenen m, van der ent ck. J Cyst Fibros. 2020 Jul;19(4):553-561. doi: 10.1016/j.jcf.2020.04.007. Epub 2020 May 30. J Cyst Fibros. 2020. PMID: 32487494 Free article.
Clinical effects of the three CFTR potentiator treatments curcumin, genistein and ivacaftor in patients with the CFTR-S1251N gating mutation.
Berkers G, van der Meer R, van Mourik P, Vonk AM, Kruisselbrink E, Suen SW, Heijerman HG, Majoor CJ, Koppelman GH, Roukema J, Janssens HM, de Rijke YB, Kemper EM, Beekman JM, van der Ent CK, de Jonge HR. Berkers G, et al. Among authors: van mourik p, van der meer r, van der ent ck. J Cyst Fibros. 2020 Nov;19(6):955-961. doi: 10.1016/j.jcf.2020.04.014. Epub 2020 Jun 1. J Cyst Fibros. 2020. PMID: 32499204 Free article. Clinical Trial.
Comparison of Organoid Swelling and In Vivo Biomarkers of CFTR Function to Determine Effects of Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for the F508del Mutation.
Graeber SY, van Mourik P, Vonk AM, Kruisselbrink E, Hirtz S, van der Ent CK, Mall MA, Beekman JM. Graeber SY, et al. Among authors: van mourik p, van der ent ck. Am J Respir Crit Care Med. 2020 Dec 1;202(11):1589-1592. doi: 10.1164/rccm.202004-1200LE. Am J Respir Crit Care Med. 2020. PMID: 32687398 No abstract available.
Protocol for Application, Standardization and Validation of the Forskolin-Induced Swelling Assay in Cystic Fibrosis Human Colon Organoids.
Vonk AM, van Mourik P, Ramalho AS, Silva IAL, Statia M, Kruisselbrink E, Suen SWF, Dekkers JF, Vleggaar FP, Houwen RHJ, Mullenders J, Boj SF, Vries R, Amaral MD, de Boeck K, van der Ent CK, Beekman JM. Vonk AM, et al. Among authors: van mourik p, van der ent ck. STAR Protoc. 2020 Jun 3;1(1):100019. doi: 10.1016/j.xpro.2020.100019. eCollection 2020 Jun 19. STAR Protoc. 2020. PMID: 33111074 Free PMC article.
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