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2008 12
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2011 2
2012 8
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350 results

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Page 1
Congenital hepatic fibrosis: case report and review of literature.
Hasbaoui BE, Rifai Z, Saghir S, Ayad A, Lamalmi N, Abilkassem R, Agadr A. Hasbaoui BE, et al. Pan Afr Med J. 2021 Feb 18;38:188. doi: 10.11604/pamj.2021.38.188.27941. eCollection 2021. Pan Afr Med J. 2021. PMID: 33995794 Free PMC article. Review.
Congenital hepatic fibrosis (CHF) is a rare autosomal recessive disease derived from biliary dysgenesis secondary to ductal plate malformation; it often coexists with Caroli's disease, von Meyenburg complexes, autosomal dominant polycystic kidney disease (ADP …
Congenital hepatic fibrosis (CHF) is a rare autosomal recessive disease derived from biliary dysgenesis secondary to du …
PKHD1 sequence variations in 78 children and adults with autosomal recessive polycystic kidney disease and congenital hepatic fibrosis.
Gunay-Aygun M, Tuchman M, Font-Montgomery E, Lukose L, Edwards H, Garcia A, Ausavarat S, Ziegler SG, Piwnica-Worms K, Bryant J, Bernardini I, Fischer R, Huizing M, Guay-Woodford L, Gahl WA. Gunay-Aygun M, et al. Mol Genet Metab. 2010 Feb;99(2):160-73. doi: 10.1016/j.ymgme.2009.10.010. Epub 2009 Oct 20. Mol Genet Metab. 2010. PMID: 19914852 Free PMC article.
PKHD1, the gene mutated in autosomal recessive polycystic kidney disease (ARPKD)/congenital hepatic fibrosis (CHF), is an exceptionally large and complicated gene that consists of 86 exons and has a number of alternatively spliced transcripts. ...
PKHD1, the gene mutated in autosomal recessive polycystic kidney disease (ARPKD)/congenital hepatic fibrosis (CHF), is …
Non-cirrhotic portal hypertension.
Sarin SK, Khanna R. Sarin SK, et al. Clin Liver Dis. 2014 May;18(2):451-76. doi: 10.1016/j.cld.2014.01.009. Clin Liver Dis. 2014. PMID: 24679506 Review.
While the long-term prognosis is generally good in NCPF, portal biliopathy and parenchymal extinction after prolonged PHT makes outcome somewhat less favorable in EHPVO. While hepatic schistosomiasis, congenital hepatic fibrosis and nodular regenerative hyper …
While the long-term prognosis is generally good in NCPF, portal biliopathy and parenchymal extinction after prolonged PHT makes outcome some …
Hepatic morphology abnormalities: beyond cirrhosis.
Mamone G, Cortis K, Sarah A, Caruso S, Miraglia R. Mamone G, et al. Abdom Radiol (NY). 2018 Jul;43(7):1612-1626. doi: 10.1007/s00261-017-1351-9. Abdom Radiol (NY). 2018. PMID: 29043403 Review.
The aim of this pictorial essay is to review the CT and MRI appearances of hepatic morphology abnormalities in the cirrhotic liver and other diseases, describing pathologic conditions that can mimic cirrhosis, with useful tips for the differential diagnosis. Mimickers of cirrhosi …
The aim of this pictorial essay is to review the CT and MRI appearances of hepatic morphology abnormalities in the cirrhotic liver and other …
Imaging of fibropolycystic liver disease.
Sharbidre K, Zahid M, Venkatesh SK, Bhati C, Lalwani N. Sharbidre K, et al. Abdom Radiol (NY). 2022 Jul;47(7):2356-2370. doi: 10.1007/s00261-022-03565-7. Epub 2022 Jun 7. Abdom Radiol (NY). 2022. PMID: 35670875 Review.
In particular, DPMs can result in various degrees of intrahepatic duct involvement and a wide spectrum of cholangiopathies, including congenital hepatic fibrosis, Caroli disease, polycystic liver disease, and Von Meyenberg complexes. ...
In particular, DPMs can result in various degrees of intrahepatic duct involvement and a wide spectrum of cholangiopathies, including con …
Congenital hepatic fibrosis.
Lorimer AR, McGee J, McAlpine SG. Lorimer AR, et al. Postgrad Med J. 1967 Dec;43(506):771-3. doi: 10.1136/pgmj.43.506.771. Postgrad Med J. 1967. PMID: 6079201 Free PMC article. No abstract available.
Congenital hepatic fibrosis.
De Vos M, Barbier F, Cuvelier C. De Vos M, et al. J Hepatol. 1988 Apr;6(2):222-8. doi: 10.1016/s0168-8278(88)80036-9. J Hepatol. 1988. PMID: 3411102
We report the clinical features of 7 men (mean age 22 years, range 7-53 years) with congenital hepatic fibrosis (CHF). Five patients presented with variceal bleeding and/or hepatosplenomegaly due to portal hypertension. ...
We report the clinical features of 7 men (mean age 22 years, range 7-53 years) with congenital hepatic fibrosis (CHF). …
Congenital hepatic fibrosis.
Hodgson HJ, Davies DR, Thompson RP. Hodgson HJ, et al. J Clin Pathol. 1976 Jan;29(1):11-6. doi: 10.1136/jcp.29.1.11. J Clin Pathol. 1976. PMID: 1249246 Free PMC article.
During 10 years four patients with congenital hepatic fibrosis were seen in a general hospital in London; three presented in adult life. ...
During 10 years four patients with congenital hepatic fibrosis were seen in a general hospital in London; three present …
Congenital hepatic fibrosis.
Hardin CA. Hardin CA. Arch Surg. 1965 Dec;91(6):884-6. doi: 10.1001/archsurg.1965.01320180018005. Arch Surg. 1965. PMID: 5294638 No abstract available.
350 results