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Activation of peroxisome proliferator-activated receptor pathway stimulates the mitochondrial respiratory chain and can correct deficiencies in patients' cells lacking its components.

Bastin J, Aubey F, Rötig A, Munnich A, Djouadi F. Bastin J, et al. Among authors: aubey f. J Clin Endocrinol Metab. 2008 Apr;93(4):1433-41. doi: 10.1210/jc.2007-1701. Epub 2008 Jan 22. J Clin Endocrinol Metab. 2008. PMID: 18211970

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Long-term follow-up of bezafibrate treatment in patients with the myopathic form of carnitine palmitoyltransferase 2 deficiency.

Bonnefont JP, Bastin J, Laforêt P, Aubey F, Mogenet A, Romano S, Ricquier D, Gobin-Limballe S, Vassault A, Behin A, Eymard B, Bresson JL, Djouadi F. Bonnefont JP, et al. Among authors: aubey f. Clin Pharmacol Ther. 2010 Jul;88(1):101-8. doi: 10.1038/clpt.2010.55. Epub 2010 May 26. Clin Pharmacol Ther. 2010. PMID: 20505667 Clinical Trial.

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Genetic basis for correction of very-long-chain acyl-coenzyme A dehydrogenase deficiency by bezafibrate in patient fibroblasts: toward a genotype-based therapy.

Gobin-Limballe S, Djouadi F, Aubey F, Olpin S, Andresen BS, Yamaguchi S, Mandel H, Fukao T, Ruiter JP, Wanders RJ, McAndrew R, Kim JJ, Bastin J. Gobin-Limballe S, et al. Among authors: aubey f. Am J Hum Genet. 2007 Dec;81(6):1133-43. doi: 10.1086/522375. Epub 2007 Oct 29. Am J Hum Genet. 2007. PMID: 17999356 Free PMC article.

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Bezafibrate increases very-long-chain acyl-CoA dehydrogenase protein and mRNA expression in deficient fibroblasts and is a potential therapy for fatty acid oxidation disorders.

Djouadi F, Aubey F, Schlemmer D, Ruiter JP, Wanders RJ, Strauss AW, Bastin J. Djouadi F, et al. Among authors: aubey f. Hum Mol Genet. 2005 Sep 15;14(18):2695-703. doi: 10.1093/hmg/ddi303. Epub 2005 Aug 22. Hum Mol Genet. 2005. PMID: 16115821

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Potential of fibrates in the treatment of fatty acid oxidation disorders: revival of classical drugs?

Djouadi F, Aubey F, Schlemmer D, Gobin S, Laforet P, Wanders RJ, Strauss AW, Bonnefont JP, Bastin J. Djouadi F, et al. Among authors: aubey f. J Inherit Metab Dis. 2006 Apr-Jun;29(2-3):341-2. doi: 10.1007/s10545-006-0266-3. J Inherit Metab Dis. 2006. PMID: 16763897

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Peroxisome proliferator activated receptor delta (PPARdelta) agonist but not PPARalpha corrects carnitine palmitoyl transferase 2 deficiency in human muscle cells.

Djouadi F, Aubey F, Schlemmer D, Bastin J. Djouadi F, et al. Among authors: aubey f. J Clin Endocrinol Metab. 2005 Mar;90(3):1791-7. doi: 10.1210/jc.2004-1936. Epub 2004 Dec 21. J Clin Endocrinol Metab. 2005. PMID: 15613406

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Knockout of insulin-like growth factor-1 receptor impairs distal lung morphogenesis.

Epaud R, Aubey F, Xu J, Chaker Z, Clemessy M, Dautin A, Ahamed K, Bonora M, Hoyeau N, Fléjou JF, Mailleux A, Clement A, Henrion-Caude A, Holzenberger M. Epaud R, et al. Among authors: aubey f. PLoS One. 2012;7(11):e48071. doi: 10.1371/journal.pone.0048071. Epub 2012 Nov 6. PLoS One. 2012. PMID: 23139760 Free PMC article.

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Humanized mouse model to study bacterial infections targeting the microvasculature.

Melican K, Aubey F, Duménil G. Melican K, et al. Among authors: aubey f. J Vis Exp. 2014 Apr 1;(86):51134. doi: 10.3791/51134. J Vis Exp. 2014. PMID: 24747976 Free PMC article.

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Assessment of the interplay between blood and skin vascular abnormalities in adult purpura fulminans.

Lerolle N, Carlotti A, Melican K, Aubey F, Pierrot M, Diehl JL, Caille V, Hékimian G, Gandrille S, Mandet C, Bruneval P, Dumenil G, Borgel D. Lerolle N, et al. Among authors: aubey f. Am J Respir Crit Care Med. 2013 Sep 15;188(6):684-92. doi: 10.1164/rccm.201302-0228OC. Am J Respir Crit Care Med. 2013. PMID: 23924269

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Inhibitors of the Neisseria meningitidis PilF ATPase provoke type IV pilus disassembly.

Aubey F, Corre JP, Kong Y, Xu X, Obino D, Goussard S, Lapeyrere C, Souphron J, Couturier C, Renard S, Duménil G. Aubey F, et al. Proc Natl Acad Sci U S A. 2019 Apr 23;116(17):8481-8486. doi: 10.1073/pnas.1817757116. Epub 2019 Apr 4. Proc Natl Acad Sci U S A. 2019. PMID: 30948644 Free PMC article.

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