A human neuronal model of Niemann Pick C disease developed from stem cells isolated from patient's skin.
Bergamin N, Dardis A, Beltrami A, Cesselli D, Rigo S, Zampieri S, Domenis R, Bembi B, Beltrami CA.
Bergamin N, et al.
Orphanet J Rare Dis. 2013 Feb 21;8:34. doi: 10.1186/1750-1172-8-34.
Orphanet J Rare Dis. 2013.
PMID: 23433359
Free PMC article.
Cells were induced to differentiate along a neuronal fate adapting methods previously described by Beltrami et al, 2007. The surface immunophenotype of stem cells was analyzed by FACS. Stem cell and neuronal markers expression were evaluated by immunofluorescence. ...
Cells were induced to differentiate along a neuronal fate adapting methods previously described by Beltrami et al, 2007. The surface …