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89 results

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Page 1
Congenital hepatic fibrosis: case report and review of literature.
Hasbaoui BE, Rifai Z, Saghir S, Ayad A, Lamalmi N, Abilkassem R, Agadr A. Hasbaoui BE, et al. Pan Afr Med J. 2021 Feb 18;38:188. doi: 10.11604/pamj.2021.38.188.27941. eCollection 2021. Pan Afr Med J. 2021. PMID: 33995794 Free PMC article. Review.
Congenital hepatic fibrosis (CHF) is a rare autosomal recessive disease derived from biliary dysgenesis secondary to ductal plate malformation; it often coexists with Caroli's disease, von Meyenburg complexes, autosomal dominant polycystic kidney disease (ADP
Congenital hepatic fibrosis (CHF) is a rare autosomal recessive disease derived from biliary dysgenesis secondary to du
Congenital hepatic fibrosis and autosomal recessive polycystic kidney disease.
Srinath A, Shneider BL. Srinath A, et al. J Pediatr Gastroenterol Nutr. 2012 May;54(5):580-7. doi: 10.1097/MPG.0b013e31824711b7. J Pediatr Gastroenterol Nutr. 2012. PMID: 22197937 Free PMC article. Review.
OBJECTIVES: The published natural history of congenital hepatic fibrosis (CHF) was examined to inform clinical decision making in autosomal recessive polycystic kidney disease (ARPKD). ...
OBJECTIVES: The published natural history of congenital hepatic fibrosis (CHF) was examined to inform clinical decision …
Imaging of fibropolycystic liver disease.
Sharbidre K, Zahid M, Venkatesh SK, Bhati C, Lalwani N. Sharbidre K, et al. Abdom Radiol (NY). 2022 Jul;47(7):2356-2370. doi: 10.1007/s00261-022-03565-7. Epub 2022 Jun 7. Abdom Radiol (NY). 2022. PMID: 35670875 Review.
In particular, DPMs can result in various degrees of intrahepatic duct involvement and a wide spectrum of cholangiopathies, including congenital hepatic fibrosis, Caroli disease, polycystic liver disease, and Von Meyenberg complexes. ...
In particular, DPMs can result in various degrees of intrahepatic duct involvement and a wide spectrum of cholangiopathies, including con
Non-cirrhotic portal hypertension.
Sarin SK, Khanna R. Sarin SK, et al. Clin Liver Dis. 2014 May;18(2):451-76. doi: 10.1016/j.cld.2014.01.009. Clin Liver Dis. 2014. PMID: 24679506 Review.
While the long-term prognosis is generally good in NCPF, portal biliopathy and parenchymal extinction after prolonged PHT makes outcome somewhat less favorable in EHPVO. While hepatic schistosomiasis, congenital hepatic fibrosis and nodular regenerative hyper …
While the long-term prognosis is generally good in NCPF, portal biliopathy and parenchymal extinction after prolonged PHT makes outcome some …
Hepatic morphology abnormalities: beyond cirrhosis.
Mamone G, Cortis K, Sarah A, Caruso S, Miraglia R. Mamone G, et al. Abdom Radiol (NY). 2018 Jul;43(7):1612-1626. doi: 10.1007/s00261-017-1351-9. Abdom Radiol (NY). 2018. PMID: 29043403 Review.
The aim of this pictorial essay is to review the CT and MRI appearances of hepatic morphology abnormalities in the cirrhotic liver and other diseases, describing pathologic conditions that can mimic cirrhosis, with useful tips for the differential diagnosis. Mimickers of cirrhosi …
The aim of this pictorial essay is to review the CT and MRI appearances of hepatic morphology abnormalities in the cirrhotic liver and other …
Experience of a single center with congenital hepatic fibrosis: a review of the literature.
Shorbagi A, Bayraktar Y. Shorbagi A, et al. World J Gastroenterol. 2010 Feb 14;16(6):683-90. doi: 10.3748/wjg.v16.i6.683. World J Gastroenterol. 2010. PMID: 20135715 Free PMC article. Review.
Congenital hepatic fibrosis (CHF) is an autosomal recessive inherited malformation defined pathologically by a variable degree of periportal fibrosis and irregularly shaped proliferating bile ducts. ...
Congenital hepatic fibrosis (CHF) is an autosomal recessive inherited malformation defined pathologically by a variable
An update on ductal plate malformations and fibropolycystic diseases of the liver.
Mirza H, Besse W, Somlo S, Weinreb J, Kenney B, Jain D. Mirza H, et al. Hum Pathol. 2023 Feb;132:102-113. doi: 10.1016/j.humpath.2022.06.022. Epub 2022 Jun 28. Hum Pathol. 2023. PMID: 35777701 Review.
Multiple clinical phenotypes in the liver are proposed to originate from ductal plate malformations: congenital hepatic fibrosis, Caroli's disease, Von Meyenburg complex, and the liver cysts of autosomal dominant polycystic kidney and liver diseases. ...
Multiple clinical phenotypes in the liver are proposed to originate from ductal plate malformations: congenital hepatic fib
Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF).
Turkbey B, Ocak I, Daryanani K, Font-Montgomery E, Lukose L, Bryant J, Tuchman M, Mohan P, Heller T, Gahl WA, Choyke PL, Gunay-Aygun M. Turkbey B, et al. Pediatr Radiol. 2009 Feb;39(2):100-11. doi: 10.1007/s00247-008-1064-x. Epub 2008 Dec 17. Pediatr Radiol. 2009. PMID: 19089418 Free PMC article. Review.
ARPKD/CHF is an inherited disease characterized by non-obstructive fusiform dilatation of the renal collecting ducts leading to enlarged spongiform kidneys and ductal plate malformation of the liver resulting in congenital hepatic fibrosis. ARPKD/CHF has a br …
ARPKD/CHF is an inherited disease characterized by non-obstructive fusiform dilatation of the renal collecting ducts leading to enlarged spo …
What is congenital hepatic fibrosis?
Desmet VJ. Desmet VJ. Histopathology. 1992 Jun;20(6):465-77. doi: 10.1111/j.1365-2559.1992.tb01031.x. Histopathology. 1992. PMID: 1607148 Review.
The hypothesis that congenital hepatic fibrosis corresponds to a fetal type of biliary fibrosis would explain a number of disparate observations. According to this concept, congenital hepatic fibrosis does not correspond to a single clini …
The hypothesis that congenital hepatic fibrosis corresponds to a fetal type of biliary fibrosis would explain a number …
89 results