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Gene expression profile study in CFTR mutated bronchial cell lines.
Gambardella S, Biancolella M, D'Apice MR, Amati F, Sangiuolo F, Farcomeni A, Chillemi G, Bueno S, Desideri A, Novelli G. Gambardella S, et al. Clin Exp Med. 2006 Dec;6(4):157-65. doi: 10.1007/s10238-006-0116-5. Clin Exp Med. 2006. PMID: 17191107
In order to identify CF modifier genes, we built a low-density home-made oligoarray containing 144 genes selected according to biochemical criteria and evaluated their expression in two CF bronchial epithelial cell lines (CuFi1 F508del/F508del; CuFi3 F …
In order to identify CF modifier genes, we built a low-density home-made oligoarray containing 144 genes selected according to biochemical c …
Gene expression profile analysis of 4-phenylbutyrate treatment of IB3-1 bronchial epithelial cell line demonstrates a major influence on heat-shock proteins.
Wright JM, Zeitlin PL, Cebotaru L, Guggino SE, Guggino WB. Wright JM, et al. Physiol Genomics. 2004 Jan 15;16(2):204-11. doi: 10.1152/physiolgenomics.00160.2003. Physiol Genomics. 2004. PMID: 14583596
The Affymetrix genome-spanning U133 microarray set was used to compare mRNA expression levels in untreated IB3-1 cell line cultures with cultures treated with 1 mM PBA for 12 and 24 h. ...Our results demonstrate the usefulness of gene expression …
The Affymetrix genome-spanning U133 microarray set was used to compare mRNA expression levels in untreated IB3-1 cell line …
Effect of CFTR modulators Elexacaftor/Tezacaftor/Ivacaftor on lipid metabolism in human bronchial epithelial cells.
Dobi D, Loberto N, Mauri L, Bassi R, Chiricozzi E, Lunghi G, Aureli M. Dobi D, et al. Glycoconj J. 2025 Feb;42(1):1-14. doi: 10.1007/s10719-024-10174-7. Epub 2025 Jan 11. Glycoconj J. 2025. PMID: 39797966
Mutations in CFTR, notably the prevalent F508del mutation, impair chloride transport, severely affecting the respiratory system and leading to recurrent infections. ...This study investigated ETI's impact on the maturation of the mutated CFTR …
Mutations in CFTR, notably the prevalent F508del mutation, impair chloride transport, severely affecting the respirator …
Pharmacological and pre-clinical safety profile of rSIV.F/HN, a hybrid lentiviral vector for cystic fibrosis gene therapy.
Moiseenko A, Sinadinos A, Sergijenko A, Pineault K, Saleh A, Nekola K, Strang N, Eleftheraki A, Boyd AC, Davies JC, Gill DR, Hyde SC, McLachlan G, Rath T, Rothe M, Schambach A, Hobbie S, Schuler M, Maier U, Thomas MJ, Mennerich D, Schmidt M, Griesenbach U, Alton EWFW, Kreuz S. Moiseenko A, et al. Eur Respir J. 2025 Jan 30;65(1):2301683. doi: 10.1183/13993003.01683-2023. Print 2025 Jan. Eur Respir J. 2025. PMID: 39174284 Free PMC article.
METHODS: Air-liquid interface cultures of primary human bronchial epithelial cells (HBECs) from CF patients (F508del/F508del), as well as a CFTR-deficient immortalised human lung epithelial cell line mimicking class I (CFTR-null) homozygous m …
METHODS: Air-liquid interface cultures of primary human bronchial epithelial cells (HBECs) from CF patients (F508del/F508del), as wel …
Host transcriptomic analysis reveals a defective intracellular environment that limits SARS-CoV-2 replication in CFTR-deficient airway epithelium.
Lagni A, Lotti V, Cecchetto R, Tonon E, Diani E, Palmisano A, Piccaluga PP, Calgaro M, Vitulo N, Sorio C, Gibellini D. Lagni A, et al. Front Cell Infect Microbiol. 2026 Mar 25;16:1754083. doi: 10.3389/fcimb.2026.1754083. eCollection 2026. Front Cell Infect Microbiol. 2026. PMID: 41959565 Free PMC article.
Cystic fibrosis (CF) is characterized by chronic airway inflammation, yet clinical observations have revealed more favorable COVID-19 outcomes than originally predicted. Several studies demonstrated a significant decrease of SARS-CoV-2 replication in CF-mutated b …
Cystic fibrosis (CF) is characterized by chronic airway inflammation, yet clinical observations have revealed more favorable COVID-19 outcom …
Double-stranded DNA donors and CRISPR-Cas9 for universal correction of mutations causing cystic fibrosis in human airway cells.
Sinha V, Ayoub PG, Juett CJ, Lathrop LE, Foley RA, Sims RA, Long JD, Duggan EC, Fernandes NR, Illek B, Gomperts BN, Jonas SJ, Kohn DB. Sinha V, et al. Mol Ther Nucleic Acids. 2026 Aug 3;37(3):103049. doi: 10.1016/j.omtn.2026.103049. eCollection 2026 Sep 8. Mol Ther Nucleic Acids. 2026. PMID: 42662918 Free PMC article.
Cystic fibrosis (CF) is a devastating genetic disease caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene. As morbidity and mortality from CF results from a lack of mucus clearance that leads to chronic bacterial infecti …
Cystic fibrosis (CF) is a devastating genetic disease caused by mutations in the cystic fibrosis transmembrane conductance regulator …