Search Page
Save citations to file
Email citations
Send citations to clipboard
Add to Collections
Add to My Bibliography
Create a file for external citation management software
Your saved search
Your RSS Feed
Search Results
7 results
Filters applied: . Clear all
Results are displayed in a computed author sort order.
The Results By Year timeline is not available.
Page 1
PPAR gamma agonist leriglitazone improves frataxin-loss impairments in cellular and animal models of Friedreich Ataxia.
Neurobiol Dis. 2021 Jan;148:105162. doi: 10.1016/j.nbd.2020.105162. Epub 2020 Nov 7.
Neurobiol Dis. 2021.
PMID: 33171227
Free article.
Frataxin-deficient cardiomyocytes present an altered thiol-redox state which targets actin and pyruvate dehydrogenase.
Purroy R, Medina-Carbonero M, Ros J, Tamarit J.
Purroy R, et al. Among authors: medina carbonero m.
Redox Biol. 2020 May;32:101520. doi: 10.1016/j.redox.2020.101520. Epub 2020 Apr 5.
Redox Biol. 2020.
PMID: 32279039
Free PMC article.
Item in Clipboard
Calcitriol increases frataxin levels and restores mitochondrial function in cell models of Friedreich Ataxia.
Britti E, Delaspre F, Sanz-Alcázar A, Medina-Carbonero M, Llovera M, Purroy R, Mincheva-Tasheva S, Tamarit J, Ros J.
Britti E, et al. Among authors: medina carbonero m.
Biochem J. 2021 Jan 15;478(1):1-20. doi: 10.1042/BCJ20200331.
Biochem J. 2021.
PMID: 33305808
Item in Clipboard
Mitochondrial iron and calcium homeostasis in Friedreich ataxia.
Tamarit J, Britti E, Delaspre F, Medina-Carbonero M, Sanz-Alcázar A, Cabiscol E, Ros J.
Tamarit J, et al. Among authors: medina carbonero m.
IUBMB Life. 2021 Mar;73(3):543-553. doi: 10.1002/iub.2457. Epub 2021 Mar 5.
IUBMB Life. 2021.
PMID: 33675183
Free article.
Review.
Item in Clipboard
Mice harboring the FXN I151F pathological point mutation present decreased frataxin levels, a Friedreich ataxia-like phenotype, and mitochondrial alterations.
Medina-Carbonero M, Sanz-Alcázar A, Britti E, Delaspre F, Cabiscol E, Ros J, Tamarit J.
Medina-Carbonero M, et al.
Cell Mol Life Sci. 2022 Jan 17;79(2):74. doi: 10.1007/s00018-021-04100-5.
Cell Mol Life Sci. 2022.
PMID: 35038030
Free PMC article.
Item in Clipboard
Mitochondrial impairment, decreased sirtuin activity and protein acetylation in dorsal root ganglia in Friedreich Ataxia models.
Sanz-Alcázar A, Britti E, Delaspre F, Medina-Carbonero M, Pazos-Gil M, Tamarit J, Ros J, Cabiscol E.
Sanz-Alcázar A, et al. Among authors: medina carbonero m.
Cell Mol Life Sci. 2023 Dec 21;81(1):12. doi: 10.1007/s00018-023-05064-4.
Cell Mol Life Sci. 2023.
PMID: 38129330
Free PMC article.
Item in Clipboard
Evolution of an Iron-Detoxifying Protein: Eukaryotic and Rickettsia Frataxins Contain a Conserved Site Which Is Not Present in Their Bacterial Homologues.
Alves R, Pazos-Gil M, Medina-Carbonero M, Sanz-Alcázar A, Delaspre F, Tamarit J.
Alves R, et al. Among authors: medina carbonero m.
Int J Mol Sci. 2022 Oct 29;23(21):13151. doi: 10.3390/ijms232113151.
Int J Mol Sci. 2022.
PMID: 36361939
Free PMC article.
Item in Clipboard
Cite
Cite